{"id":102797,"date":"2025-05-30T00:00:00","date_gmt":"2025-05-29T22:00:00","guid":{"rendered":"https:\/\/dev.institutchiaribcn.com\/comunicacion\/novo-artigo-cientifico-sobre-a-sindrome-neuro-cranio-vertebral-associada-a-sindrome-de-ehlers-danlos\/"},"modified":"2025-12-01T11:07:09","modified_gmt":"2025-12-01T10:07:09","slug":"novo-artigo-cientifico-sindrome-neuro-cranio-vertebral-associada-sindrome-ehlers-danlos","status":"publish","type":"comunicacion","link":"https:\/\/institutchiaribcn.com\/pt\/novo-artigo-cientifico-sindrome-neuro-cranio-vertebral-associada-sindrome-ehlers-danlos\/","title":{"rendered":"Novo artigo cient\u00edfico sobre a S\u00edndrome Neuro-Cr\u00e2nio-Vertebral associada \u00e0 S\u00edndrome de Ehlers-Danlos"},"content":{"rendered":"<p class=\"text-muted aniview centerTXT\">Published by <a title=\"Artigos de ICSEB\" href=\"https:\/\/institutchiaribcn.com\/pt\/author\/chiari\/\" rel=\"author\">ICSEB<\/a> at 30 Maio, 2025<\/p>\n<p><strong>A S\u00edndrome de Ehlers-Danlos (EDS)<\/strong> inclui um grupo complexo de dist\u00farbios heterog\u00eaneos, de car\u00e1ter heredit\u00e1rio, caracterizados pela fragilidade e aumento da elasticidade dos tecidos conjuntivos moles, o que nos interessa especialmente <strong>no tipo associado \u00e0 patologia vertebral e \u00e0 instabilidade cr\u00e2nio-cervical.<\/strong><\/p>\n<p><em>Qual \u00e9 a rela\u00e7\u00e3o entre a S\u00edndrome de Ehlers-Danlos (EDS) e a S\u00edndrome Neuro-Cr\u00e2nio-Vertebral (SNCV)?<\/em><\/p>\n<p><em>Eliminar a tra\u00e7\u00e3o do Filum terminale atrav\u00e9s do tratamento do Filum System\u00ae pode ajudar pacientes com Ehlers-Danlos associado \u00e0 SNCV?<\/em><\/p>\n<p>O novo artigo <strong>\u201cNeuro-Cranio-Vertebral Syndrome Associated with Ehlers\u2013Danlos Syndrome: Diagnosis and Treatment\u201d,<\/strong> publicado por <strong>Miguel B. Royo-Salvador, Marco V. Fiallos-Rivera e Horia C. Salca,<\/strong> tenta responder a essas perguntas, propondo faz\u00ea-lo por meio da teoria da S\u00edndrome Neuro-Cr\u00e2nio-Vertebral em rela\u00e7\u00e3o \u00e0 disfun\u00e7\u00e3o do col\u00e1geno no Filum terminale causada pela EDS e o consequente tratamento.<\/p>\n<p>Na publica\u00e7\u00e3o na Biomed, considera-se que a elasticidade na coluna vertebral causa um alongamento maior do que o do Filum terminale, o que esgota este \u00faltimo e resulta em uma tra\u00e7\u00e3o caudal do Sistema Nervoso central; originando assim uma S\u00edndrome Neuro-Cr\u00e2nio-Vertebral.<\/p>\n<p>Os autores descrevem pela primeira vez os resultados observados em um grupo de pacientes operados no ICSEB com o duplo diagn\u00f3stico de EDS e SNCV, em compara\u00e7\u00e3o com um grupo de pacientes com apenas SNCV.<\/p>\n<p>Segundo os autores, os pacientes da amostra com EDS e SNCV apresentaram mais sintomas cranianos e vertebrais do que o outro grupo. Tamb\u00e9m foram observadas diferen\u00e7as significativas nos sinais neurol\u00f3gicos presentes nos pacientes com EDS-SNCV em compara\u00e7\u00e3o com aqueles com apenas SNCV. Al\u00e9m disso, <strong>os pacientes submetidos \u00e0 sec\u00e7\u00e3o do filum terminale (SFT) com a t\u00e9cnica minimamente invasiva do Filum System\u00ae mostraram uma melhora significativa nos sinais e sintomas<\/strong> (Fig.1).<\/p>\n<p><img decoding=\"async\" class=\"aligncenter\" src=\"https:\/\/institutchiaribcn.com\/wp-content\/uploads\/2025\/05\/mejorias-improvements-eds-sft-icseb.jpg\" \/><\/p>\n<p>Royo et Al. destacam como <strong>o conceito de instabilidade cr\u00e2nio-cervical devido \u00e0 EDS, portanto, n\u00e3o explica uma grande quantidade de sinais e sintomas neurol\u00f3gicos, os quais parecem se encaixar melhor na teoria da tra\u00e7\u00e3o exercida pelo Filum Terminale sobre <\/strong>todo o Sistema Nervoso Central na SNCV.<\/p>\n<p>\u201c<strong>O tratamento cir\u00fargico implicaria apenas a sec\u00e7\u00e3o do filum terminale<\/strong>, enquanto a fus\u00e3o cervical jamais estaria justificada nesses pacientes\u201d, relatam nossos pesquisadores na <strong>conclus\u00e3o do estudo.<\/strong><\/p>\n<p>Agradecemos \u00e0 <strong>Chiari &amp; Scoliosis &amp; Syringomyelia Foundation<\/strong> por continuar apoiando as pesquisas do nosso <strong>Departamento de P+D,<\/strong> e a este \u00faltimo por realizar mais um estudo t\u00e3o interessante!<\/p>\n<p><span style=\"text-align: justify;\">Podem encontrar o <strong>artigo completo<\/strong> em: <a href=\"https:\/\/institutchiaribcn.com\/pt\/neuro-cranio-vertebral-syndrome-associated-with-ehlers-danlos-syndrome-diagnosis-and-treatment\/\">https:\/\/institutchiaribcn.com\/pt\/neuro-cranio-vertebral-syndrome-associated-with-ehlers-danlos-syndrome-diagnosis-and-treatment\/<\/a><\/span><\/p>\n<p style=\"text-align: justify;\">E <strong>mais informa\u00e7\u00f5es sobre a EDS<\/strong> em: <a href=\"https:\/\/institutchiaribcn.com\/pt\/sindrome-de-ehlers-danlos\/\">https:\/\/institutchiaribcn.com\/pt\/sindrome-de-ehlers-danlos\/\u00a0<\/a><\/p>\n","protected":false},"featured_media":102798,"template":"","tipos-de-comunicacion":[533],"class_list":["post-102797","comunicacion","type-comunicacion","status-publish","has-post-thumbnail","hentry","tipos-de-comunicacion-comunicados"],"yoast_head":"<!-- This site is optimized with the Yoast SEO plugin v27.1.1 - https:\/\/yoast.com\/product\/yoast-seo-wordpress\/ -->\n<title>S\u00edndromes Neuro-Cr\u00e2nio-Vertebral e Ehlers-Danlos | ICSEB<\/title>\n<meta name=\"description\" content=\"A S\u00edndrome de Ehlers-Danlos (EDS) inclui um grupo complexo de dist\u00farbios heterog\u00eaneos, de car\u00e1ter heredit\u00e1rio, caracterizados... \u00a0 Ver mais \u2192\" \/>\n<meta name=\"robots\" content=\"index, follow, max-snippet:-1, max-image-preview:large, max-video-preview:-1\" \/>\n<link rel=\"canonical\" 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