{"id":117479,"date":"1998-06-17T00:00:29","date_gmt":"1998-06-16T22:00:29","guid":{"rendered":"https:\/\/dev.institutchiaribcn.com\/siringomielia-malformaciones-de-la-union-craneo-cervical-y-malformaciones-raquiespinales\/"},"modified":"2026-03-30T10:21:01","modified_gmt":"2026-03-30T08:21:01","slug":"siringomielia-malformaciones-de-la-union-craneo-cervical-y-malformaciones-raquiespinales","status":"publish","type":"publicaciones","link":"https:\/\/institutchiaribcn.com\/jp\/siringomielia-malformaciones-de-la-union-craneo-cervical-y-malformaciones-raquiespinales\/","title":{"rendered":"Siringomielia, malformaciones de la uni\u00f3n cr\u00e1neo-cervical y malformaciones raquiespinales"},"content":{"rendered":"<p class=\"text-muted aniview centerTXT\">Published by <a title=\"Entradas de ICSEB\" href=\"https:\/\/institutchiaribcn.com\/jp\/author\/chiari\/\" rel=\"author\">ICSEB<\/a> at 1998\u5e746\u670817\u65e5<\/p>\n<p style=\"text-align: center;\">Medicine 1998; 7(97): 4512-4519<\/p>\n<p style=\"text-align: center;\">A. Miralles Mart\u00ednez, F. Gonz\u00e1lez Llanos*, A. Isla Guerrero* y E. D\u00edez Tejedor<br \/>\nServicios de Neurolog\u00eda y de *Neurocirug\u00eda.<br \/>\nHospital Universitario La Paz. Universidad Aut\u00f3noma de Madrid.<\/p>\n<p><strong>Cita bibliogr\u00e1fica:<\/strong><\/p>\n<p style=\"text-align: justify;\">Una hip\u00f3tesis reciente y ambiciosa intenta explicar por un mismo mecanismo enfermedades como la siringomielia, la malformaci\u00f3n de Arnold-Chiari, la impresi\u00f3n basilar y la escoliosis idiop\u00e1tica. Para Royo-Salvador, su autor, que se basa en los trabajos de Roth10, Barry11y Williams, el motivo princeps ser\u00eda un desarrollo embrionario con un anclaje medular bajo12. Establece como nivel normal del cono medular hasta L1 (94% del grupo control), presentando un nivel m\u00e1s bajo en el 84,2% del de pacientes con siringomielia.<\/p>\n<p style=\"text-align: justify;\">Recordemos que a partir del tercer mes de desarrollo es cuando el neurorraquis empieza a crecer m\u00e1s r\u00e1pidamenteque el neuroeje. Si el anclaje del cono medular es bajo producir\u00eda una fuerza de tracci\u00f3n medular que desencadenar\u00eda unos mecanismos de compensaci\u00f3n intentando evitar el da\u00f1o medular. Estos mecanismos compensatorios afectar\u00edan al raquis produciendo una adaptaci\u00f3n de la columna vertebral, lo que ocasionar\u00eda una escoliosis; tambi\u00e9n se producir\u00eda una tracci\u00f3n sobre el basicondrocr\u00e1neo mediada por la tensi\u00f3n que transmite la m\u00e9dula al troncoenc\u00e9falo, dando lugar a alteraciones como la platibasia, la impresi\u00f3n basilar y deformidades en el di\u00e1metro del agujero occipital.<\/p>\n<p style=\"text-align: justify;\">Cuando los mecanismos de compensaci\u00f3n del raquis son insuficientes- empezar\u00eda a afectarse el neuroeje con descenso de las am\u00edgdalas cerebelosas y del troncoenc\u00e9falo. Si prosigue la tracci\u00f3n medular se producir\u00eda una transmisi\u00f3n de dicha fuerza que da\u00f1ar\u00eda la m\u00e9dula. Recordemos que la regi\u00f3n centromedular tiene una irrigaci\u00f3n terminal sin anastomosis lo que hace especialmente sensible a la isquemia.<\/p>\n<p style=\"text-align: justify;\">La tensi\u00f3n ejercida sobre la m\u00e9dula ocasionar\u00eda un colapso de los vasos terminales en el centro medular, necrosando \u00e1reas centromedulares donde se crear\u00eda una cavidad rellena del material proteico residual que por mecanismos osm\u00f3ticos atraer\u00eda l\u00edquido a su interior. Los mecanismos hidrodin\u00e1micos actuar\u00edan en paralelo debido a la implantaci\u00f3n de las am\u00edgdalas cerebelosas en el agujero magno.<\/p>\n<p style=\"text-align: justify;\">Para este autor, la siringomielia idiop\u00e1tica ser\u00eda la manifestaci\u00f3n neurol\u00f3gica de una enfermedad plurimorfopatol\u00f3gica que se expresa como malformaci\u00f3n de Arnold-Chiari, escoliosis idiop\u00e1tica, impresi\u00f3n basilar, platibasia y cavitaciones intramedulares entre otras, debidas a una asincron\u00eda del crecimiento del neuroeje-neurorraquis.<\/p>\n<p style=\"text-align: center;\"><a class=\"btn btn-default fade-hover\" href=\"https:\/\/institutchiaribcn.com\/commons\/pdf\/publicaciones\/otros-autores\/siringomielia-malformaciones-union-craneo-cervical-malformaciones-raquiespinales_98.pdf\" target=\"_blank\" rel=\"noopener\"> \u30c0\u30a6\u30f3\u30ed\u30fc\u30c9<\/a><\/p>\n","protected":false},"featured_media":0,"template":"","tipos-de-publicaciones":[633],"class_list":["post-117479","publicaciones","type-publicaciones","status-publish","hentry","tipos-de-publicaciones-633"],"yoast_head":"<!-- This site is optimized with the Yoast SEO plugin v27.1.1 - https:\/\/yoast.com\/product\/yoast-seo-wordpress\/ -->\n<title>\u810a\u9ac4\u7a7a\u6d1e\u75c7\u3068\u982d\u84cb\u9838\u690e\u5947\u5f62\u8a3a\u65ad\u6cbb\u7642 | \u30d0\u30eb\u30bb\u30ed\u30ca\u30ad\u30a2\u30ea\u7814\u7a76\u6240<\/title>\n<meta name=\"description\" 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