{"id":78006,"date":"2025-05-23T00:00:00","date_gmt":"2025-05-22T22:00:00","guid":{"rendered":"https:\/\/dev.institutchiaribcn.com\/comunicacion\/levolution-de-la-cavite-syringomyelique-et-de-la-scoliose-idiopathique-10-ans-apres-lapplication-du-filum-system\/"},"modified":"2026-03-18T10:42:39","modified_gmt":"2026-03-18T09:42:39","slug":"levolution-de-la-cavite-syringomyelique-et-de-la-scoliose-idiopathique-10-ans-apres-lapplication-du-filum-system","status":"publish","type":"comunicacion","link":"https:\/\/institutchiaribcn.com\/fr\/levolution-de-la-cavite-syringomyelique-et-de-la-scoliose-idiopathique-10-ans-apres-lapplication-du-filum-system\/","title":{"rendered":"L\u2019\u00e9volution de la cavit\u00e9 syringomy\u00e9lique et de la scoliose idiopathique, 10 ans apr\u00e8s l\u2019application du Filum System\u00ae"},"content":{"rendered":"<p class=\"text-muted aniview centerTXT\">Published by <a title=\"Articles par ICSEB\" href=\"https:\/\/institutchiaribcn.com\/fr\/author\/chiari\/\" rel=\"author\">ICSEB<\/a> at 23 mai, 2025<\/p>\n<p style=\"text-align: justify;\"><strong>Cas 18015<\/strong><\/p>\n<p style=\"text-align: justify;\"><strong>Diagnostic<\/strong> : Syndrome Neuro-cr\u00e2nio-vert\u00e9bral, Maladie du filum. Descente des amygdales c\u00e9r\u00e9belleuses (Syndrome d\u2019Arnold-Chiari I). Syringomy\u00e9lie et scoliose idiopathiques.<\/p>\n<p style=\"text-align: justify;\"><strong>Date l\u2019 intervention<\/strong> de Section du Filum terminale (SFT): <strong>avril 2015<\/strong><\/p>\n<p style=\"text-align: justify;\"><strong>La patiente n\u00ba 18015<\/strong>, qui souhaite rester anonyme mais nous a donn\u00e9 son consentement pour la publication de son cas, <strong>a \u00e9t\u00e9 op\u00e9r\u00e9e selon la m\u00e9thode Filum System\u00ae dans notre centre, \u00e0 l\u2019\u00e2ge de 7 ans, en 2015<\/strong>.<\/p>\n<p style=\"text-align: justify;\"><strong>\u00a0<\/strong><strong>Avant l\u2019intervention, ses IRM du 25\/03\/2015 d\u00e9montraient : <\/strong>Maladie du filum et Syndrome Neuro-cr\u00e2nio-vert\u00e9bral avec descente des amygdales c\u00e9r\u00e9belleuses (Syndrome d\u2019Arnold-Chiari I), syringomy\u00e9lie et scoliose idiopathiques. La t\u00e9l\u00e9m\u00e9trie du rachis montrait : scoliose dextroconvexe au niveau dorsal et l\u00e9voconvexe au niveau lombaire, ainsi qu\u2019une rectification de la lordose cervicale.<\/p>\n<p style=\"text-align: justify;\">Dans son dossier m\u00e9dical, d\u00e8s le contr\u00f4le de la premi\u00e8re ann\u00e9e postop\u00e9ratoire, une diminution de la cavit\u00e9 intram\u00e9dullaire avait \u00e9t\u00e9 not\u00e9e, qui s\u2019est encore am\u00e9lior\u00e9e au cours des ann\u00e9es suivantes, jusqu\u2019\u00e0 aujourd\u2019hui, lorsque C. vient \u00e0 l\u2019ICSEB pour son contr\u00f4le \u00e0 10 ans.<\/p>\n<p style=\"text-align: justify;\"><strong>Lors de son suivi comparatif par IRM, on peut observer :<\/strong><\/p>\n<p style=\"text-align: justify;\">Sur le plan clinique, la patiente a am\u00e9lior\u00e9 certains sympt\u00f4mes d\u00e8s la <strong>premi\u00e8re ann\u00e9e postop\u00e9ratoire<\/strong>, d\u2019autres sont rest\u00e9s stables et certains ont disparu ; tandis que lors de son examen neurologique, la r\u00e9cup\u00e9ration de certains signes a \u00e9t\u00e9 not\u00e9e, avec la persistance d\u2019autres signes inchang\u00e9s.<\/p>\n<p style=\"text-align: justify;\">Actuellement, \u00e0 17 ans et lors du <strong>contr\u00f4le postop\u00e9ratoire \u00e0 10 ans, <\/strong>C<strong>. rapporte ne plus pr\u00e9senter la majorit\u00e9 des sympt\u00f4mes pr\u00e9op\u00e9ratoires (90 %), et le sp\u00e9cialiste souligne la r\u00e9cup\u00e9ration de la majorit\u00e9 des signes neurologiques, ainsi que la nette diminution de la cavit\u00e9 intram\u00e9dullaire et la disparition de la courbure scoliotique.<\/strong><\/p>\n<p style=\"text-align: justify;\"><strong>Le Filum System\u00ae a pour objectif d\u2019arr\u00eater la d\u00e9t\u00e9rioration et l\u2019\u00e9volution de la Maladie du Filum<\/strong> et des diagnostics associ\u00e9s \u2014 comme on peut le constater ici concernant la descente des amygdales c\u00e9r\u00e9belleuses, qui dans ce cas reste inchang\u00e9e.<\/p>\n<p style=\"text-align: justify;\">Cependant, <strong>dans la plupart des cas, des r\u00e9sultats meilleurs que pr\u00e9vu<\/strong> sont obtenus, puisque l\u2019on observe une am\u00e9lioration et un soulagement d\u2019une grande partie des sympt\u00f4mes et signes chez la majorit\u00e9 des patients ; et chez certains, <strong>aussi la r\u00e9versibilit\u00e9 des l\u00e9sions visibles aux examens compl\u00e9mentaires, comme on peut le voir dans ce cas.<\/strong><\/p>\n","protected":false},"featured_media":78007,"template":"","tipos-de-comunicacion":[510],"class_list":["post-78006","comunicacion","type-comunicacion","status-publish","has-post-thumbnail","hentry","tipos-de-comunicacion-nouvelles"],"yoast_head":"<!-- This site is optimized with the Yoast SEO plugin v27.1.1 - https:\/\/yoast.com\/product\/yoast-seo-wordpress\/ -->\n<title>\u00c9volution syringomy\u00e9lie &amp; scoliose 10 ans | ICSEB<\/title>\n<meta name=\"description\" content=\"R\u00e9sultats 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