{"id":77991,"date":"2025-05-30T00:00:00","date_gmt":"2025-05-29T22:00:00","guid":{"rendered":"https:\/\/dev.institutchiaribcn.com\/comunicacion\/nouvel-article-scientifique-sur-le-syndrome-neuro-cranio-vertebral-associe-au-syndrome-dehlers-danlos\/"},"modified":"2026-03-06T12:05:06","modified_gmt":"2026-03-06T11:05:06","slug":"nouvel-article-scientifique-sur-le-syndrome-neuro-cranio-vertebral-associe-au-syndrome-dehlers-danlos","status":"publish","type":"comunicacion","link":"https:\/\/institutchiaribcn.com\/fr\/nouvel-article-scientifique-sur-le-syndrome-neuro-cranio-vertebral-associe-au-syndrome-dehlers-danlos\/","title":{"rendered":"Nouvel article scientifique sur le Syndrome Neuro-Cr\u00e2nio-Vert\u00e9bral associ\u00e9 au Syndrome d\u2019Ehlers-Danlos"},"content":{"rendered":"<p class=\"text-muted aniview centerTXT\">Published by <a title=\"Articles par ICSEB\" href=\"https:\/\/institutchiaribcn.com\/fr\/author\/chiari\/\" rel=\"author\">ICSEB<\/a> at 30 mai, 2025<\/p>\n<p style=\"text-align: justify;\"><strong>Le Syndrome d\u2019Ehlers-Danlos (EDS)<\/strong> regroupe un ensemble complexe de troubles h\u00e9t\u00e9rog\u00e8nes d\u2019origine h\u00e9r\u00e9ditaire, caract\u00e9ris\u00e9s par la fragilit\u00e9 et l\u2019\u00e9lasticit\u00e9 accrue des tissus conjonctifs mous. Il nous concerne particuli\u00e8rement dans sa forme associ\u00e9e \u00e0 une<strong> pathologie vert\u00e9brale et une instabilit\u00e9 cr\u00e2nio-cervicale<\/strong>.<\/p>\n<p style=\"text-align: justify;\"><em>Quelle est la relation entre le Syndrome d\u2019Ehlers-Danlos (EDS) et le Syndrome Neuro-Cr\u00e2nio-Vert\u00e9bral (SNCV)?<\/em><\/p>\n<p style=\"text-align: justify;\"><em>L\u2019\u00e9limination de la traction du Filum terminale par le biais du traitement Filum System\u00ae peut-il aider les patients atteints de EDS associ\u00e9 \u00e0 un SNCV?<\/em><\/p>\n<p style=\"text-align: justify;\">Le nouvel article <strong>\u201cNeuro-Cranio-Vertebral Syndrome Associated with Ehlers\u2013Danlos Syndrome: Diagnosis and Treatment\u201d<\/strong>, publi\u00e9 par Miguel B. Royo-Salvador, Marco V. Fiallos-Rivera et Horia C. Salca, tente de r\u00e9pondre \u00e0 ces questions en proposant la th\u00e9orie du Syndrome Neuro-Cr\u00e2nio-Vert\u00e9bral en lien avec une dysfonction du collag\u00e8ne au niveau du Filum terminale due au EDS, et le traitement qui en d\u00e9coule.<\/p>\n<p style=\"text-align: justify;\">La publication dans Biomed indique que l\u2019\u00e9lasticit\u00e9 de la colonne vert\u00e9brale entra\u00eene un allongement sup\u00e9rieur \u00e0 celui du Filum terminale, ce qui conduit \u00e0 son \u00e9puisement et \u00e0 une traction caudale du syst\u00e8me nerveux central, provoquant ainsi un syndrome Neuro-cr\u00e2nio-vert\u00e9bral.<\/p>\n<p style=\"text-align: justify;\">Les auteurs d\u00e9crivent pour la premi\u00e8re fois les r\u00e9sultats observ\u00e9s chez un groupe de patients op\u00e9r\u00e9s \u00e0 l\u2019ICSEB avec un double diagnostic de EDS et SNCV, compar\u00e9s \u00e0 un groupe de patients atteints uniquement de SNCV.<\/p>\n<p style=\"text-align: justify;\">Selon les auteurs, les patients pr\u00e9sentant le double diagnostic EDS + SNCV pr\u00e9sentaient davantage de sympt\u00f4mes cr\u00e2niens et vert\u00e9braux que l\u2019autre groupe. Des diff\u00e9rences significatives ont \u00e9galement \u00e9t\u00e9 observ\u00e9es dans les signes neurologiques chez les patients EDS-SNCV par rapport \u00e0 ceux atteints uniquement de SNCV. En outre, <strong>les patients ayant subi une section du filum terminale (SFT) selon la technique mini-invasive du Filum System\u00ae ont montr\u00e9 une am\u00e9lioration significative des signes et sympt\u00f4mes<\/strong> (Fig.1).<\/p>\n<p style=\"text-align: justify;\">Royo et Al. soulignent que <strong>le concept d\u2019instabilit\u00e9 cr\u00e2nio-cervicale li\u00e9e au EDS n\u2019explique pas un grand nombre de signes et sympt\u00f4mes neurologiques, qui semblent en revanche mieux correspondre \u00e0 la th\u00e9orie de la traction transmise par le Filum terminale<\/strong> \u00e0 l\u2019ensemble du syst\u00e8me nerveux central dans le cadre du SNCV.<\/p>\n<p style=\"text-align: justify;\">\u00ab\u00a0<strong>Le traitement chirurgical impliquerait uniquement la section du filum terminale<\/strong>, tandis qu\u2019une fusion cervicale ne serait jamais justifi\u00e9e chez ces patients.\u00bb<br \/>\nrapportent nos chercheurs en <strong>conclusion de l\u2019\u00e9tude<\/strong>.<\/p>\n<p style=\"text-align: justify;\">Nous remercions la <strong>Chiari &amp; Scoliosis &amp; Syringomyelia Foundation<\/strong> pour son soutien continu \u00e0 la recherche men\u00e9e par notre <strong>D\u00e9partement R+D+i<\/strong>, ainsi que ce dernier pour avoir r\u00e9alis\u00e9 une autre \u00e9tude aussi int\u00e9ressante !<\/p>\n<p style=\"text-align: justify;\">Vous pouvez consulter <strong>l\u2019article complet<\/strong> ici :<br \/>\n<a href=\"https:\/\/institutchiaribcn.com\/fr\/pathologie-vertebrale-syndrome-dehlers-danlos-cause-traitement-selon-filum-system\/\"> https:\/\/institutchiaribcn.com\/neuro-cranio-vertebral-syndrome-associated-with-ehlers-danlos-syndrome-diagnosis-and-treatment\/<\/a><br \/>\nEt <strong>plus d\u2019informations sur le EDS<\/strong> ici :<br \/>\n<a href=\"https:\/\/institutchiaribcn.com\/sindrome-de-ehlers-danlos-filum-system\/\">https:\/\/institutchiaribcn.com\/sindrome-de-ehlers-danlos-filum-system\/<\/a><\/p>\n","protected":false},"featured_media":77992,"template":"","tipos-de-comunicacion":[510],"class_list":["post-77991","comunicacion","type-comunicacion","status-publish","has-post-thumbnail","hentry","tipos-de-comunicacion-nouvelles"],"yoast_head":"<!-- This site is optimized with the Yoast SEO plugin v27.1.1 - https:\/\/yoast.com\/product\/yoast-seo-wordpress\/ -->\n<title>Syndrome neuro\u2011cranio\u2011vert\u00e9bral &amp; Ehlers\u2011Danlos | ICSEB<\/title>\n<meta name=\"description\" content=\"Nouvel article explorant le lien entre syndrome neuro\u2011cranio\u2011vert\u00e9bral et syndrome d\u2019Ehlers\u2011Danlos, avec implications cliniques.\" \/>\n<meta name=\"robots\" content=\"index, follow, max-snippet:-1, max-image-preview:large, max-video-preview:-1\" \/>\n<link rel=\"canonical\" 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