{"id":77961,"date":"2025-07-04T00:00:00","date_gmt":"2025-07-03T22:00:00","guid":{"rendered":"https:\/\/dev.institutchiaribcn.com\/comunicacion\/levolution-favorable-dun-cas-de-syndrome-darnold-chiari-i-et-de-syringomyelie-idiopathique-a-7-ans-apres-lapplication-du-filum-system\/"},"modified":"2026-03-09T10:19:21","modified_gmt":"2026-03-09T09:19:21","slug":"levolution-favorable-dun-cas-de-syndrome-darnold-chiari-i-et-de-syringomyelie-idiopathique-a-7-ans-apres-lapplication-du-filum-system","status":"publish","type":"comunicacion","link":"https:\/\/institutchiaribcn.com\/fr\/levolution-favorable-dun-cas-de-syndrome-darnold-chiari-i-et-de-syringomyelie-idiopathique-a-7-ans-apres-lapplication-du-filum-system\/","title":{"rendered":"L\u2019\u00e9volution favorable d\u2019un cas de Syndrome d\u2019Arnold Chiari I et de Syringomy\u00e9lie Idiopathique, \u00e0 7 ans apr\u00e8s l\u2019application du Filum System\u00ae"},"content":{"rendered":"<p class=\"text-muted aniview centerTXT\">Published by <a title=\"Articles par ICSEB\" href=\"https:\/\/institutchiaribcn.com\/fr\/author\/chiari\/\" rel=\"author\">ICSEB<\/a> at 4 juillet, 2025<\/p>\n<p style=\"text-align: justify;\"><strong>Cas 19475<\/strong><\/p>\n<p style=\"text-align: justify;\"><strong>Diagnostic:<\/strong> Syndrome Neuro-cr\u00e2nio-vert\u00e9bral. Maladie du Filum. Descente des amygdales c\u00e9r\u00e9belleuses (Syndrome d\u2019Arnold-Chiari I). Kyste intram\u00e9dullaire (Syringomy\u00e9lie idiopathique).<\/p>\n<p style=\"text-align: justify;\"><strong>Date de l\u2019intervention: <\/strong>Section du Filum Terminale (SFT) selon Filum System<sup>\u00ae<\/sup>: Avril 2018.<\/p>\n<p style=\"text-align: justify;\">La patiente, qui souhaite rester anonyme, a \u00e9t\u00e9 op\u00e9r\u00e9e \u00e0 l\u2019\u00e2ge de 11 ans et est revenue faire plusieurs contr\u00f4les dans notre centre, le dernier <strong>apr\u00e8s 7 ans de l\u2019intervention, au d\u00e9but de l\u2019ann\u00e9e 2025.<\/strong><\/p>\n<p>Avant l\u2019application du traitement, elle souffrait cliniquement surtout de <strong>c\u00e9phal\u00e9es, d\u2019instabilit\u00e9 et de vertiges, ainsi que d\u2019une fatigue g\u00e9n\u00e9ralis\u00e9e et facile.<\/strong><\/p>\n<p>Sur ses images d\u2019IRM pr\u00e9op\u00e9ratoires de 2017 (Fig.1), on pouvait observer, entre autres constatations :<\/p>\n<p><strong>\u00c0 partir du contr\u00f4le \u00e0 un mois, puis \u00e0 un an (2019), et lors de tous les suivis suivants (2023 et 2024), une am\u00e9lioration globale de tous les sympt\u00f4mes a \u00e9t\u00e9 constat\u00e9e, jusqu\u2019\u00e0 la disparition de presque tous lors de la derni\u00e8re visite (2025).<\/strong> Il en va de m\u00eame pour l\u2019examen neurologique<strong>, avec la r\u00e9cup\u00e9ration de la majorit\u00e9 des signes cliniques objectifs.<\/strong><\/p>\n<p>Dans ce cas, on peut <strong>\u00e9galement observer sur les images d\u2019IRM une am\u00e9lioration progressive de l\u2019\u00e9tat de la patiente apr\u00e8s l\u2019intervention<\/strong>, comme le montrent les Figures 2, 3 et 4.<\/p>\n<p>Ici, nous pr\u00e9sentons comme premi\u00e8re image de chaque comparaison de contr\u00f4le, les IRM de 2019, qui \u00e9taient encore inchang\u00e9es par rapport aux pr\u00e9op\u00e9ratoires de 2017 \u2014 dans la plupart des cas, il faut attendre quelques ann\u00e9es avant de pouvoir observer des am\u00e9liorations sur les images.<\/p>\n<p>C\u2019est \u00e0 partir des IRM de contr\u00f4le de 2023, cinq ans apr\u00e8s l\u2019intervention, que nous avons la preuve d\u2019une am\u00e9lioration \u00e9vidente visible sur chacune des images, encore plus marqu\u00e9e lors du dernier contr\u00f4le, <strong>fin 2024, \u00e0 sept ans, avec<\/strong> :<\/p>\n<p><strong>\u2013\u00a0\u00a0\u00a0 L\u2019ascension des amygdales c\u00e9r\u00e9belleuses et la normalisation du \u00a0\u00a0\u00a0quatri\u00e8me ventricule <\/strong>(Fig. 2)<strong>.<\/strong><\/p>\n<p>Nous sommes ravis de l\u2019excellent r\u00e9sultat du traitement dans le cas mentionn\u00e9 de cette patiente, qui peut maintenant, \u00e0 l\u2019\u00e2ge de 18 ans, profiter de l\u2019opportunit\u00e9 qu\u2019elle a eue de lib\u00e9rer la moelle \u00e9pini\u00e8re de la traction caus\u00e9e par le filum terminale. Nous lui souhaitons de rester dans cet \u00e9tat actuel.<\/p>\n<p style=\"text-align: justify;\"><strong>Le Filum System\u00ae stoppe l\u2019\u00e9volution du syndrome d\u2019Arnold-Chiari de type I et de la syringomy\u00e9lie idiopathique ; il favorise la restauration des l\u00e9sions r\u00e9versibles du syst\u00e8me nerveux et am\u00e9liore la qualit\u00e9 de vie des patients.<\/strong><\/p>\n","protected":false},"featured_media":77962,"template":"","tipos-de-comunicacion":[510],"class_list":["post-77961","comunicacion","type-comunicacion","status-publish","has-post-thumbnail","hentry","tipos-de-comunicacion-nouvelles"],"yoast_head":"<!-- This site is optimized with the Yoast SEO plugin v27.1.1 - https:\/\/yoast.com\/product\/yoast-seo-wordpress\/ -->\n<title>\u00c9volution favorable du Chiari I et de la syringomy\u00e9lie | ICSEB<\/title>\n<meta name=\"description\" content=\"Cas clinique d\u2019Arnold-Chiari I et de syringomy\u00e9lie idiopathique avec \u00e9volution favorable 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