{"id":77931,"date":"2025-09-28T00:00:00","date_gmt":"2025-09-27T22:00:00","guid":{"rendered":"https:\/\/dev.institutchiaribcn.com\/comunicacion\/septembre-mois-de-sensibilisation-au-syndrome-darnold-chiarinous-clarifions-les-doutessur-le-syndrome-de-type-i-et-son-approche-par-le-filum-system\/"},"modified":"2026-04-02T10:29:25","modified_gmt":"2026-04-02T08:29:25","slug":"septembre-mois-de-sensibilisation-au-syndrome-darnold-chiarinous-clarifions-les-doutessur-le-syndrome-de-type-i-et-son-approche-par-le-filum-system","status":"publish","type":"comunicacion","link":"https:\/\/institutchiaribcn.com\/fr\/septembre-mois-de-sensibilisation-au-syndrome-darnold-chiarinous-clarifions-les-doutessur-le-syndrome-de-type-i-et-son-approche-par-le-filum-system\/","title":{"rendered":"Septembre : mois de sensibilisation au syndrome d\u2019Arnold-ChiariNOUS CLARIFIONS LES DOUTESsur le syndrome de type I et son approche par le Filum System\u00ae"},"content":{"rendered":"<p style=\"text-align: justify;\">Comme chaque ann\u00e9e, durant le mois de septembre, nous nous consacrons \u00e0 la <strong>sensibilisation au Syndrome d\u2019Arnold-Chiari<\/strong>. Le <strong>28 septembre<\/strong> est c\u00e9l\u00e9br\u00e9e sa <strong>Journ\u00e9e Internationale<\/strong>, avec pour objectif de donner de la visibilit\u00e9 \u00e0 cette maladie et d\u2019apporter un soutien aux personnes atteintes ainsi qu\u2019\u00e0 leurs familles.<\/p>\n<p style=\"text-align: justify;\">Comme il est bien connu, notre Institut propose aux patients une <strong>m\u00e9thode de traitement unique de cette pathologie, en l\u2019abordant gr\u00e2ce \u00e0 notre technique chirurgicale exclusive, mini-invasive<\/strong>. Celle-ci permet ensuite de restaurer les l\u00e9sions et fonctions du syst\u00e8me nerveux affect\u00e9 \u2013 dans la mesure o\u00f9 elles sont r\u00e9versibles et r\u00e9cup\u00e9rables \u2013 \u00e0 l\u2019aide de <strong>r\u00e9\u00e9ducation et de traitements m\u00e9dicamenteux<\/strong>.<\/p>\n<p style=\"text-align: justify;\">La d\u00e9couverte \u00e9tiologique du Dr Royo consid\u00e8re qu\u2019un <strong>ligament, le<\/strong>\u00a0<strong>filum terminale<\/strong>, <strong>trop tendu de mani\u00e8re cong\u00e9nitale, est \u00e0 l\u2019origine d\u2019une traction excessive sur l\u2019ensemble du syst\u00e8me nerveux central (SNC), ce qui constitue la\u00a0<\/strong><strong>Maladie du Filum (MF)<\/strong><strong>. L\u2019une de ses cons\u00e9quences, entre autres, est la descente de tout le SNC \u2013 et de sa portion inf\u00e9rieure la plus visible, les\u00a0<\/strong><strong>amygdales c\u00e9r\u00e9belleuses<\/strong><strong>\u00a0\u2013 \u00e0 travers le trou occipital, une descente<\/strong> caract\u00e9ristique du syndrome.<\/p>\n<p style=\"text-align: justify;\">Actuellement, la Maladie du Filum est souvent confondue avec la\u00a0moelle attach\u00e9e occulte\u00a0(MAO) ou non occulte (MA), qui sont deux types de dysraphismes. \u00c0 ce sujet, nous souhaitons profiter du mois de sensibilisation pour\u00a0clarifier certaines confusions.<\/p>\n<p style=\"text-align: justify;\">M\u00eame si <strong>le terme\u00a0\u00ab\u00a0<\/strong><strong>dysraphism<em>\u00a0\u00bb se<\/em><\/strong><strong>\u00a0d\u00e9signe un groupe de malformations cong\u00e9nitales r\u00e9sultant d\u2019un d\u00e9faut de fermeture du tube neural pendant le d\u00e9veloppement embryonnaire<\/strong> \u2013 et que, pour cette raison, la <strong>MF<\/strong> pourrait \u00eatre inscrite dans cette cat\u00e9gorie \u2013, celle-ci consiste plus pr\u00e9cis\u00e9ment en un\u00a0conflit m\u00e9canique entre l\u2019axe neural et la colonne vert\u00e9brale, caus\u00e9 par une croissance asynchrone excessive durant la phase embryonnaire.<\/p>\n<p style=\"text-align: justify;\">Nous estimons que cette <strong>croissance asynchrone, associ\u00e9e au conflit m\u00e9canique mentionn\u00e9, est provoqu\u00e9e par un <\/strong><strong>filum terminale apparemment normal<\/strong>, responsable de plusieurs pathologies, dont la principale \u2013 selon nos \u00e9tudes et nos bases de donn\u00e9es \u2013 est le\u00a0<strong>syndrome d\u2019Arnold-Chiari I<\/strong>, provoqu\u00e9 par une traction caudale qui entra\u00eene vers le bas l\u2019ensemble du SNC.<\/p>\n<p style=\"text-align: justify;\"><strong>Contrairement \u00e0 la MA et \u00e0 la MAO<\/strong>, o\u00f9 le filum terminale peut ancrer la moelle \u00e0 diff\u00e9rents niveaux de mani\u00e8re visible sur les IRM \u2013 et qui sont des entit\u00e9s diff\u00e9rentes du Chiari I \u2013, ce dernier ne pr\u00e9sente\u00a0aucune preuve d\u2019ancrage m\u00e9dullaire. En revanche, le paradigme pos\u00e9 par <strong>la d\u00e9finition de la MF contribue \u00e0\u00a0<\/strong><strong>expliquer la descente des amygdales c\u00e9r\u00e9belleuses<\/strong><strong>\u00a0en tant que simple cons\u00e9quence m\u00e9canique, les deux entit\u00e9s \u00e9tant \u00e9troitement li\u00e9es : la maladie du Filum \u00e9tant la cause, le syndrome de Chiari I sa cons\u00e9quence.<\/strong><\/p>\n<p style=\"text-align: justify;\">Cela\u00a0ouvre de nouvelles perspectives de recherche\u00a0et \u00e9largit les options th\u00e9rapeutiques disponibles pour les patients, en leur <strong>offrant une m\u00e9thode qui agit sur la\u00a0<\/strong><strong>cause<\/strong><strong>, et non uniquement sur les\u00a0<\/strong><strong>sympt\u00f4mes<\/strong><strong>\u00a0de la pathologie, avec un faible risque chirurgical.<\/strong><\/p>\n<p style=\"text-align: justify;\">En \u00e9liminant la cause, le SNC n\u2019est plus soumis \u00e0 une traction caudale constante, et peut ainsi r\u00e9parer et restaurer les l\u00e9sions survenues avant le traitement, <strong>ce qui am\u00e9liore la qualit\u00e9 de vie dans la majorit\u00e9 des cas.<\/strong><\/p>\n<p style=\"text-align: justify;\"><strong>Diffuser cette d\u00e9couverte et d\u2019autres r\u00e9sultats de notre \u00e9quipe contribue \u00e0 sensibiliser de plus en plus le public au syndrome d\u2019Arnold-Chiari I<\/strong>, et \u00e0 redonner de l\u2019espoir aux patients et \u00e0 leurs proches. Rejoignez-nous dans cette d\u00e9marche !<\/p>\n<p style=\"text-align: justify;\">Vous pouvez trouver toutes les informations utiles ici :<\/p>\n<p style=\"text-align: justify;\"><a href=\"https:\/\/institutchiaribcn.com\/fr\/articles-dr-royo\/\">https:\/\/institutchiaribcn.com\/fr\/articles-dr-royo\/<\/a><\/p>\n<p style=\"text-align: justify;\"><a href=\"https:\/\/institutchiaribcn.com\/fr\/faqs\/\">https:\/\/institutchiaribcn.com\/fr\/faqs\/<\/a><\/p>\n<p style=\"text-align: justify;\"><a href=\"https:\/\/institutchiaribcn.com\/fr\/maladies-que-nous-traitons\/arnold-chiari-syndrome\/\">https:\/\/institutchiaribcn.com\/fr\/maladies-que-nous-traitons\/arnold-chiari-syndrome\/<\/a><\/p>\n","protected":false},"featured_media":143941,"template":"","tipos-de-comunicacion":[510],"class_list":["post-77931","comunicacion","type-comunicacion","status-publish","has-post-thumbnail","hentry","tipos-de-comunicacion-nouvelles"],"yoast_head":"<!-- This site is optimized with the Yoast SEO plugin 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