{"id":15074,"date":"2026-03-20T00:00:53","date_gmt":"2026-03-19T23:00:53","guid":{"rendered":"https:\/\/dev.institutchiaribcn.com\/enfermedades\/malaltia-cerebrovascular-leucoaraiosi\/"},"modified":"2026-04-10T09:56:47","modified_gmt":"2026-04-10T07:56:47","slug":"malaltia-cerebrovascular-leucoaraiosi","status":"publish","type":"enfermedades","link":"https:\/\/institutchiaribcn.com\/ca\/malaltia-cerebrovascular-leucoaraiosi\/","title":{"rendered":"Malaltia cerebrovascular"},"content":{"rendered":"<p><strong>\u00daltima actualizaci\u00f3n: 20\/03\/2026, <\/strong><a href=\"https:\/\/institutchiaribcn.com\/ca\/personal-clinic\/\" target=\"_blank\" rel=\"noopener noreferrer\"><strong>Dr. Miguel B. Royo Salvador<\/strong><\/a>, <strong>Numero colegiado 10389.<\/strong> <strong>Neurocirujano y Neur\u00f3logo.<\/strong><\/p>\n<h2><strong>Definici\u00f3<\/strong><\/h2>\n<p style=\"text-align: justify;\">En general, <strong>la malaltia cerebrovascular<\/strong> \u00e9s una definici\u00f3 que s\u2019utilitza per a descriure un grup heterogeni de condicions patol\u00f2giques de les quals la caracter\u00edstica comuna \u00e9s la <strong>disfunci\u00f3 focal del teixit cerebral,<\/strong> per un desequilibri entre l\u2019aportaci\u00f3 i els requeriments d\u2019oxigen i altres substrats. Defineix el proc\u00e9s de manera general, sigui agut o cr\u00f2nic, isqu\u00e8mic o hemorr\u00e0gic.<\/p>\n<p>El 1987, Hachinski va introduir el concepte de <strong>Leucoaraiosi <\/strong>(del grec <em>leuko<\/em> = blanc i <em>araios <\/em>= rarefacci\u00f3) per referir-se a una alteraci\u00f3 en les imatges de la Tomografia Computada i de la Resson\u00e0ncia Nuclear Magn\u00e8tica (RMN) cerebral en la subst\u00e0ncia blanca dels hemisferis cerebrals. Les lesions poden ser punctiformes o m\u00e9s extenses, focals o difoses. Amb aquest terme no va proposar cap correlaci\u00f3 cl\u00ednica o patol\u00f2gica, tan sols va donar nom a unes imatges anormals relativament freq\u00fcents. Es tracta per tant d\u2019un terme de neuroimatge descriptiu que pot associar-se a diferents situacions cl\u00edniques i patol\u00f2giques, i heterogeni perqu\u00e8 inclou diversos tipus d\u2019alteracions morfol\u00f2giques.<\/p>\n<p>La subst\u00e0ncia blanca rep la seva aportaci\u00f3 sangu\u00ednia d\u2019un complex sistema de microvasculaci\u00f3 cerebral, format per petites arterioles penetrants que sorgeixen de les principals art\u00e8ries cerebrals, formant angles rectes. Es tracta d\u2019art\u00e8ries terminals que s\u00f3n de gran longitud i mida petita. A causa d\u2019aix\u00f2, la subst\u00e0ncia blanca al voltant dels ventricles (periventricular) es converteix en una zona de vascularitzaci\u00f3 lim\u00edtrof, el que la fa particularment susceptible a patir lesions per isqu\u00e8mia. L\u2019afectaci\u00f3 d\u2019aquestes arterioles, en les que s\u2019origina un estretament i disminuci\u00f3 de la llum arterial, produiria una disminuci\u00f3 de l\u2019aportaci\u00f3 sangu\u00ednia, que de manera cr\u00f2nica seria la responsable de la pres\u00e8ncia de la leucoaraiosi.<\/p>\n<p>La progressi\u00f3 de la leucoaraiosi tendeix a seguir un patr\u00f3 general. Inicialment s\u2019observen les lesions periventriculars a la zona del marge (barrets) dels ventricles laterals (<em>Fig. 1)<\/em> estenent-se, en relaci\u00f3 amb la severitat del fenomen, al voltant d\u2019ells (<em>Fig. 2). <\/em><\/p>\n<div class=\"row\">\n<div class=\"col-md-6\" style=\"margin-bottom: 10px;\" align=\"center\"><a href=\"https:\/\/institutchiaribcn.com\/wp-content\/uploads\/2019\/05\/cerebro-vascular.png\"><img decoding=\"async\" class=\"alignnone size-full wp-image-8736\" src=\"https:\/\/institutchiaribcn.com\/wp-content\/uploads\/2019\/05\/cerebro-vascular.png\" alt=\"\" width=\"auto\" height=\"350\" \/><\/a><br \/>\nFig.1<\/div>\n<div class=\"col-md-6\" style=\"margin-bottom: 10px;\" align=\"center\"><a href=\"https:\/\/institutchiaribcn.com\/wp-content\/uploads\/2019\/05\/cerbero-vascular-enfermedad.png\"><img decoding=\"async\" class=\"alignnone size-full wp-image-8737\" src=\"https:\/\/institutchiaribcn.com\/wp-content\/uploads\/2019\/05\/cerbero-vascular-enfermedad.png\" alt=\"\" width=\"auto\" height=\"350\" \/><\/a><br \/>\nFig.2<\/div>\n<\/div>\n<p>&nbsp;<\/p>\n<hr \/>\n<h2><strong>Graus i s\u00edmptomes<\/strong><\/h2>\n<p style=\"text-align: justify;\">Malgrat ser un concepte descriptiu, la Leucoaraiosi no comporta s\u00edmptomes en s\u00ed mateixa, per\u00f2 els seus diversos graus de neuroimatge s\u2019associen a diversos quadres simptomatol\u00f2gics correlatius.<\/p>\n<p>En general, els s\u00edmptomes associats en certa mesura a qualsevol dels seus graus, poden ser: <strong>ictus isqu\u00e8mic, trastorns cognitius, claudicaci\u00f3 de la marxa, alteracions an\u00edmiques i dels esf\u00ednters. <\/strong><\/p>\n<p>Els <strong>graus de Leucoaraoiosi<\/strong> van des del <strong>grau 0 al III:<\/strong><\/p>\n<p>els <strong>graus 0 i I<\/strong> s\u00f3n lleus i sense una correspond\u00e8ncia reconeguda amb s\u00edmptomes espec\u00edfics.<\/p>\n<p>El <strong>grau II, i molt m\u00e9s el III, <\/strong>s\u00f3n greus, es consideren com la leucoaraiosi que m\u00e9s afectaci\u00f3 produeix en la subst\u00e0ncia blanca del teixit cerebral i danya a ambd\u00f3s hemisferis cerebrals, amb lesions disperses en \u00e0mplies zones del cervell; \u00e9s una malaltia que es torna progressiva. Es detecta sobretot en les persones amb algun trastorn mental, i en aquelles que pateixen malalties associades a danys neurol\u00f2gics o amb s\u00edmptomes de dem\u00e8ncia.<\/p>\n<p>&nbsp;<\/p>\n<hr \/>\n<h2><strong>Diagn\u00f2stic<\/strong><\/h2>\n<p style=\"text-align: justify;\">Tal com hem esmentat, la Leucoaraiosi es refereix a unes alteracions que es poden detectar mitjan\u00e7ant les imatges de la <strong>Tomografia Axial Computada (TAC) i per Resson\u00e0ncia Nuclear Magn\u00e8tica (RM) cerebral, <\/strong>que consisteixen en zones d\u2019hipodensitat o d\u2019hiperintensitat, respectivament.<\/p>\n<p>Entre les dues, la <strong>Imatge per RM de l\u2019enc\u00e8fal (IRM)<\/strong> que inclou seq\u00fc\u00e8ncies ponderades en T2 i FLAIR, \u00e9s la t\u00e8cnica m\u00e9s estesa en la valoraci\u00f3 de la Leucoaraiosi.<\/p>\n<p>L\u2019<strong>escala qualitativa de Fazekas <\/strong>(<em>Fig. 3) <\/em>\u00e9s la m\u00e9s utilitzada per determinar la magnitud de les lesions de la subst\u00e0ncia blanca en IRM, classificant:<\/p>\n<p>&#8211; <strong>Grau 0<\/strong>: abs\u00e8ncia de lesi\u00f3;<br \/>\n&#8211; <strong>Grau 1<\/strong>: exist\u00e8ncia de lesions focals;<br \/>\n&#8211; <strong>Grau 2<\/strong>: inici de la conflu\u00e8ncia de lesions;<br \/>\n&#8211; <strong>Grau 3<\/strong>: lesions difuses que comprenen regions senceres.<\/p>\n<div align=\"center\"><a href=\"https:\/\/institutchiaribcn.com\/wp-content\/uploads\/2019\/05\/fazekas-scale.jpg\"><img decoding=\"async\" class=\"img-responsive\" src=\"https:\/\/institutchiaribcn.com\/wp-content\/uploads\/2019\/05\/fazekas-scale.jpg\" alt=\"\" \/><\/a><br \/>\nFig.3 La escala cualitativa de Fazekas*.<\/div>\n<p><strong>&#8211; Segons el Filum System<sup>\u00ae<\/sup>:<\/strong><\/p>\n<p style=\"text-align: justify;\">Al nostre centre detectem sovint la pres\u00e8ncia d\u2019imatges de Leucoaraiosi de la subst\u00e0ncia blanca en les seq\u00fc\u00e8ncies axials en T2 de RM, especialment de grau 1 i rarament del 2, en pacients diagnosticats de patologies del conjunt de la <a href=\"https:\/\/institutchiaribcn.com\/enfermedad-del-filum\/\"><strong>Malaltia del Filum o S\u00edndrome Neuro-Cranio-Vertebral<\/strong><\/a> &#8211; almenys en el 45% de la nostra base de dades i en totes les franges d\u2019edat-.<\/p>\n<p>&nbsp;<\/p>\n<hr \/>\n<h2><strong>Causes<\/strong><\/h2>\n<p style=\"text-align: justify;\">Actualment, la patog\u00e8nesi de la Leucoaraiosi \u00e9s controvertida.<\/p>\n<p>Alguns autors recorden que encara no est\u00e0 clar si els mecanismes que produeixen els focus punctiformes isqu\u00e8mics s\u00f3n els mateixos que generen la Leucoaraiosi difosa estesa. A m\u00e9s a m\u00e9s, es desconeix si els canvis patol\u00f2gics associats s\u00f3n la causa o la conseq\u00fc\u00e8ncia de les lesions de la subst\u00e0ncia blanca.<\/p>\n<p>Les dues hip\u00f2tesis principals es refereixen a: <strong>les anomalies del flux d\u2019autoregulaci\u00f3 de la sang o a la fallada de la barrera hemato-encef\u00e0lica. <\/strong><\/p>\n<p>El mecanisme de producci\u00f3 m\u00e9s reconegut actualment, quant a la causa de Leucoaraiosi, \u00e9s la <strong>isqu\u00e8mia cr\u00f2nica per afectaci\u00f3 de les art\u00e8ries perforants. <\/strong><\/p>\n<p>La hipertensi\u00f3 arterial i altres patologies que afecten el flux sanguini i a l\u2019oxigen que aporten al cervell, semblen estar estretament relacionades amb la Leucoaraiosi greu.<\/p>\n<p><strong>&#8211; Segons el Filum System<sup>\u00ae<\/sup>:<\/strong><\/p>\n<p>Arran de l\u2019observaci\u00f3 de l\u2019associaci\u00f3 de Leucoaraiosi i focus isqu\u00e8mics punctiformes, a nivell radiol\u00f2gic, en pacients amb la <strong>Malaltia del Filum i la S\u00edndrome Neuro-Cranio-Vertebral,<\/strong> al nostre centre tenim en compte una altra hip\u00f2tesi de patog\u00e8nesi: la Leucoaraiosi podria tamb\u00e9 estar relacionada amb <strong>la tracci\u00f3 de la medul\u00b7la espinal, <\/strong>exercida per un Filum Terminale massa tens, i amb la isqu\u00e8mia que pot provocar en els teixits de tot el sistema nervi\u00f3s en provocar el col\u00b7lapse dels vasos sanguinis de menor di\u00e0metre.<\/p>\n<p>&nbsp;<\/p>\n<hr \/>\n<h2><strong>Factors de risc<\/strong><\/h2>\n<p style=\"text-align: justify;\">En general, per una banda, els factors de risc reconeguts per a la <strong>malaltia cerebrovascular<\/strong> concerneixen <strong>les caracter\u00edstiques familiars, individuals i l\u2019estil de vida. <\/strong><\/p>\n<p><strong>\u00a0<\/strong>Per altra banda, els principals factors de risc reconeguts per a la pres\u00e8ncia de <strong>Leucoaraiosi <\/strong> s\u00f3n l\u2019<strong>edat i la hipertensi\u00f3 arterial, <\/strong>encara tamb\u00e9 s\u2019associa a d\u2019altres, com <strong>Diabetes Mellitus, malalties card\u00edaques o estenosis arterials, <\/strong>que estarien associats a alteracions en la microcirculaci\u00f3 cerebral, el que condueix a una desmielinitzaci\u00f3 d\u2019origen vascular que podria considerar-se com l\u2019origen dels focus isqu\u00e8mics.<\/p>\n<p>La Leucoaraiosi est\u00e0 tamb\u00e9 relacionada amb <strong>la tercera edat<\/strong> i amb quadres de <strong>dem\u00e8ncia senil<\/strong>, encara que ha arribat a ser detectada en persones relativament joves, de 40 anys, per\u00f2 les quals el seu consum de drogues- com l\u2019<strong>hero\u00efna, el tabac i l\u2019exposici\u00f3 constant a elements contaminants-, <\/strong>les fan propenses a presentar Leucoaraiosi en qualsevol dels seus graus. Tamb\u00e9 l\u2019<strong>arteriosclerosi <\/strong>\u00e9s un altre dels factors observats en la seva aparici\u00f3.<\/p>\n<p><strong>&#8211; Segons el Filum System<sup>\u00ae<\/sup><\/strong>:<\/p>\n<p>En els pacients amb imatges de Leuroaraiosi en la subst\u00e0ncia blanca i associades a la Malaltia del Filum i la S\u00edndrome Neuro-Cranio-Vertebral, podem observar que un factor de risc com\u00fa de les dues condicions s\u00f3n els <strong>antecedents familiars: <\/strong><\/p>\n<p>&#8211; La tracci\u00f3 caudal produ\u00efda per un Filum Terminale excessivament tens, que definim com Malaltia del Filum, pot causar el mecanisme de falta de rec sanguini en la medul\u00b7la espinal, aix\u00ed com en tot el sistema nervi\u00f3s. Es tracta d\u2019una patologia de tipus cong\u00e8nit, que es pot transmetre entre familiars.<\/p>\n<p>&nbsp;<\/p>\n<hr \/>\n<h2><strong>Complicacions<\/strong><\/h2>\n<p style=\"text-align: justify;\">L\u2019entitat de la Leucoaraiosi s\u2019associa cada vegada m\u00e9s amb el <strong>deteriorament cognitiu o canvis del comportament <\/strong>dels pacients. Les manifestacions cl\u00edniques en relaci\u00f3 amb les funcions cognitives associades van des de l\u2019afectaci\u00f3 lleu fins a l\u2019aparici\u00f3 de la <strong>dem\u00e8ncia, <\/strong>i afecten fonamentalment a la <strong>velocitat de processament cognitiu i a les funcions executives. <\/strong><\/p>\n<p>&nbsp;<\/p>\n<hr \/>\n<h2><strong>Tractament<\/strong><\/h2>\n<p style=\"text-align: justify;\">Generalment, els tractaments adequats que s\u00f3n efica\u00e7os per aturar la progressi\u00f3 de Leucoaraiosi s\u00f3n diferents dels recomanats per a les malalties a les quals s\u2019associa.<\/p>\n<p>El tractament m\u00e9s indicat per alentir el seu deteriorament, sent la Leucoaraiosi progressiva, una vegada que es presenta, \u00e9s mantenir una dieta equilibrada; amb una ingesta d\u2019aliments rics en \u00e0cid f\u00f2lic, folats i vitamines del complex B i evitar subst\u00e0ncies t\u00f2xiques i estils de vida poc saludables.<\/p>\n<p><strong>&#8211; Segons el Filum System<sup>\u00ae<\/sup><\/strong>:<\/p>\n<p>Davant del fet que la Leucoaraiosi es presenta freq\u00fcentment en pacients afectats de la <a href=\"https:\/\/institutchiaribcn.com\/ca\/malaltia-del-filum\/\">Malaltia del Filum<\/a> (MF), al nostre centre, en pacients que tinguin RM encef\u00e0liques amb focus isqu\u00e8mics de la subst\u00e0ncia blanca, realitzem el protocol diagn\u00f2stic del <strong>Filum System<sup>\u00ae<\/sup><\/strong>, per detectar una possible Malaltia del Filum. Quan es confirma una tracci\u00f3 an\u00f2mala del Filum Terminale per MF, aleshores es procedeix al tractament de la Secci\u00f3 Del Filum Terminale (SFT) amb la t\u00e8cnica mini-invasiva exclusiva. En diferents casos, s\u2019ha observat la disminuci\u00f3 de la Leucoaraiosi posterior a la SFT, avalant aix\u00f2 encara m\u00e9s que una causa de la mateixa podria ser la tracci\u00f3 an\u00f2mala del sistema nervi\u00f3s.<\/p>\n<p>&nbsp;<\/p>\n<hr \/>\n<p><!--\n\n\n<h2><strong>Resultats<\/strong><\/h2>\n\n\n&nbsp;\n\n\n<p style=\"text-align: justify;\">S\u2019aporta un exemple de cas operat per la Malaltia del Filum de Secci\u00f3 del Filum Terminale, en el qual la Leucoaraiosi que s\u2019observava anteriorment ha disminu\u00eft despr\u00e9s de la cirurgia, sense altres factors coneguts que hagin pogut contribuir al canvi que s\u2019ha detectat.<\/p>\n\n\n&nbsp;\n\n\n\n<hr \/>\n\n\n\n--><\/p>\n<h2><strong>Refer\u00e8ncies bibliogr\u00e0fiques<\/strong><\/h2>\n<ol>\n<li style=\"font-size: 16px; font-weight: 300; text-align: justify;\">John Conklin, Frank L. Silver, David J. Mikulis, Daniel M. Mandell. Are acute infarcts the cause of leukoaraiosis? Brain mapping for 16 consecutive weeks. Annals of Neurology, 2014; DOI: 10.1002\/ana.24285.<\/li>\n<li style=\"font-size: 16px; font-weight: 300; text-align: justify;\">Hachinski V.C., Potter P., Merskey H: Leuko-araiosis, Arch Neurol. 1987; 44: 21-23.<\/li>\n<li style=\"font-size: 16px; font-weight: 300; text-align: justify;\">Revista Habanera de Ciencias M\u00e9dicas, versi\u00f3n On-line ISSN 1729-519X.Rev haban cienc m\u00e9d vol.12 no.3 Ciudad de La Habana jul.-set. 2013, CIENCIAS CL\u00cdNICAS Y PATOL\u00d3GICAS.<\/li>\n<li style=\"font-size: 16px; font-weight: 300; text-align: justify;\">Dr. Miguel B. Royo Salvador (1996), <a href=\"https:\/\/institutchiaribcn.com\/pdf\/publicaciones\/dr-royo\/Siringomielia-escoliosis-malformacion-Arnold_Chiari-idiopatica.pdf\" target=\"_blank\" rel=\"noopener noreferrer\"><strong>Siringomielia<\/strong>, <strong>escoliosis<\/strong> y malformaci\u00f3n de <strong>Arnold-Chiari<\/strong> idiop\u00e1ticas, etiolog\u00eda com\u00fan (PDF).<\/a> REV NEUROL (Barc); 24 (132): 937-959.<\/li>\n<li style=\"font-size: 16px; font-weight: 300; text-align: justify;\">Dr. Miguel B. Royo Salvador (1996), <a href=\"https:\/\/institutchiaribcn.com\/pdf\/publicaciones\/dr-royo\/platibasia-impresion-basilar-retroceso-odontoideo.pdf\" target=\"_blank\" rel=\"noopener noreferrer\"><strong>Platibasia<\/strong>, impresi\u00f3n basilar, retroceso odontoideo y kinking del tronco cerebral, etiolog\u00eda com\u00fan con la <strong>siringomielia<\/strong>, <strong>escoliosis<\/strong> y <strong>malformaci\u00f3n de Arnold-Chiari<\/strong> idiop\u00e1ticas (PDF).<\/a> REV NEUROL (Barc); 24 (134): 1241-1250<\/li>\n<li style=\"font-size: 16px; font-weight: 300; text-align: justify;\">Dr. Miguel B. Royo Salvador (1997), <a href=\"https:\/\/institutchiaribcn.com\/pdf\/publicaciones\/dr-royo\/Nuevo-tratamiento-sirignomielia-escoliosis-malformacion-Arnold_Chiari.pdf \" target=\"_blank\" rel=\"noopener noreferrer\">Nuevo tratamiento quir\u00fargico para la <strong>siringomielia<\/strong>, la <strong>escoliosis<\/strong>, la <strong>malformaci\u00f3n de Arnold-Chiari<\/strong>, el kinking del tronco cerebral, el retroceso odontoideo, la impresi\u00f3n basilar y la platibasia idiop\u00e1ticas (PDF).<\/a> REV NEUROL; 25 (140): 523-530<\/li>\n<li style=\"font-size: 16px; font-weight: 300; text-align: justify;\">M. B. Royo-Salvador, J. Sol\u00e9-Llenas, J. M. Dom\u00e9nech, and R. Gonz\u00e1lez-Adrio, (2005) <a href=\"https:\/\/institutchiaribcn.com\/pdf\/publicaciones\/dr-royo\/results-filum-in-20-patients.pdf \" target=\"_blank\" rel=\"noopener noreferrer\">&#8220;Results of the section of the <strong>filum terminale<\/strong> in 20 patients with <strong>syringomyelia<\/strong>, scoliosis and <strong>Chiari malformation<\/strong>&#8220;.(PDF).<\/a> Acta Neurochir (Wien) 147: 515\u2013523.<\/li>\n<li style=\"font-size: 16px; font-weight: 300; text-align: justify;\">M. B. Royo-Salvador (2014), <a href=\"https:\/\/institutchiaribcn.com\/commons\/pdf\/publicaciones\/dr-royo\/filum-system-bibliography.pdf\" target=\"_blank\" rel=\"noopener noreferrer\">&#8220;Filum System<sup>\u00ae<\/sup> Bibliography&#8221; (PDF).<\/a><\/li>\n<li style=\"font-size: 16px; font-weight: 300; text-align: justify;\">M. B. Royo-Salvador (2014), <a href=\"https:\/\/institutchiaribcn.com\/filum-system-guia-breve\/\" target=\"_blank\" rel=\"noopener noreferrer\">&#8220;Filum System<sup>\u00ae<\/sup> Gu\u00eda Breve&#8221;.<\/a><\/li>\n<\/ol>\n<p>&nbsp;<\/p>\n<hr \/>\n<p>* Imatge:<a href=\"http:\/\/www.radiologyassistant.nl\/en\/p43dbf6d16f98d\/dementia-role-of-mri.html\/\" target=\"_blank\" rel=\"noopener noreferrer\"> http:\/\/www.radiologyassistant.nl\/en\/p43dbf6d16f98d\/dementia-role-of-mri.html\/<\/a><\/p>\n","protected":false},"featured_media":1553,"template":"","class_list":["post-15074","enfermedades","type-enfermedades","status-publish","has-post-thumbnail","hentry"],"yoast_head":"<!-- This site is optimized with the Yoast SEO plugin v27.4 - https:\/\/yoast.com\/product\/yoast-seo-wordpress\/ -->\n<title>Malaltia cerebrovascular | Institut Chiari Barcelona<\/title>\n<meta name=\"description\" content=\"Malaltia cerebrovascular \u00e9s una definici\u00f3 que es fa servir per descriure un grup 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