{"id":15058,"date":"2026-03-19T00:00:53","date_gmt":"2026-03-18T23:00:53","guid":{"rendered":"https:\/\/dev.institutchiaribcn.com\/enfermedades\/sindrome-darnold-chiari-i\/"},"modified":"2026-03-30T13:20:12","modified_gmt":"2026-03-30T11:20:12","slug":"malalties-sindrome-arnold-chiari","status":"publish","type":"enfermedades","link":"https:\/\/institutchiaribcn.com\/ca\/malalties-sindrome-arnold-chiari\/","title":{"rendered":"S\u00edndrome d\u2019Arnold Chiari I"},"content":{"rendered":"<p><strong>\u00daltima actualitzaci\u00f3: 19\/03\/2026, <\/strong><a href=\"https:\/\/institutchiaribcn.com\/ca\/personal-clinic\/\" target=\"_blank\" rel=\"noopener noreferrer\"><strong>Dr. Miguel B. Royo Salvador<\/strong><\/a>, <strong>N\u00famero col\u00b7legiat 10389.<\/strong> <strong>Neurocirurgi\u00e0 i Neur\u00f2leg.<\/strong><\/p>\r\n<h2><strong>Definici\u00f3<\/strong><\/h2>\r\n<p><strong>La s\u00edndrome d&#8217;Arnold-Chiari I<\/strong> consisteix en l&#8217;herniaci\u00f3 de la part inferior de l&#8217;enc\u00e8fal \u2014les am\u00edgdales cerebel\u00b7loses\u2014 i la part inferior del cerebel pel forat occipital cap al canal vertebral, sense altres malformacions associades a la medul\u00b7la espinal. Per a alguns, el descens de les am\u00edgdales cerebel\u00b7loses ha de ser superior a 5 mm, per a altres de 3 mm, per a alguns pot ser de 0 mm, o am\u00edgdales impactades amb un quadre cl\u00ednic compatible.<\/p>\r\n<div align=\"center\"><img fetchpriority=\"high\" decoding=\"async\" class=\"size-full wp-image-7931 aligncenter\" src=\"https:\/\/institutchiaribcn.com\/wp-content\/uploads\/2019\/01\/descenso-amigdalar.jpg\" alt=\"\" width=\"298\" height=\"346\" \/><\/div>\r\n<p><em>Figura 1.- Esquema que mostra el descens amigdalar i el conseg\u00fcent augment de l&#8217;espai supracerebel\u00f3 s, en despla\u00e7ar-se tot el cerebel cap al canal vertebral, a la s\u00edndrome d&#8217;Arnold-Chiari I.<\/em><\/p>\r\n<hr \/>\r\n<h2><strong>S\u00edmptomes<\/strong><\/h2>\r\n<p>&nbsp;<\/p>\r\n<p style=\"text-align: justify;\">La cl\u00ednica de la s\u00edndrome d&#8217;Arnold-Chiari I (SACHI) pot expressar-se en diversos quadres de combinacions de s\u00edmptomes, dels quals els m\u00e9s freq\u00fcents en la nostra casu\u00edstica s\u00f3n (de m\u00e9s a menys pres\u00e8ncia): <strong>cefalea, cervic\u00e0lgies, par\u00e8sia a les extremitats, alteraci\u00f3 de la visi\u00f3, dolor a les extremitats, parest\u00e8sies, alteraci\u00f3 de la sensibilitat, v\u00e8rtigs, alteraci\u00f3 de la degluci\u00f3, lumb\u00e0lgies, deteriorament de la mem\u00f2ria, marxa alterada, dors\u00e0lgies, alteraci\u00f3 de l&#8217;equilibri, disest\u00e8sies, trastorn del llenguatge, alteraci\u00f3 d&#8217;esf\u00ednters, insomni, v\u00f2mits, p\u00e8rdua de la consci\u00e8ncia, tremolor.<\/strong><\/p>\r\n<p>&nbsp;<\/p>\r\n<hr \/>\r\n<h2><strong>Tipus de s\u00edndrome d&#8217;Arnold-Chiari<\/strong><\/h2>\r\n<p>&nbsp;<\/p>\r\n<div align=\"center\"><img decoding=\"async\" class=\"img-thumbnail size-full wp-image-1575 aligncenter\" src=\"https:\/\/institutchiaribcn.com\/wp-content\/uploads\/2015\/05\/tension_filum_terminale_02.jpg\" alt=\"arnold chiari - tension_filum_terminale_02\" width=\"250\" height=\"260\" \/><\/div>\r\n<p>Hi ha quatre tipus cl\u00e0ssics (I, II, III, IV) i dos (&#8220;0&#8221;, &#8220;1,5&#8221;) que s&#8217;han descrit recentment:<\/p>\r\n<p><strong>Tipus I.<\/strong> Descens de les am\u00edgdales cerebel\u00b7loses sense cap altra malformaci\u00f3 del Sistema Nervi\u00f3s (SN).<\/p>\r\n<p><strong>Tipus II.<\/strong> Descens de les am\u00edgdales cerebel\u00b7loses amb malformaci\u00f3 neurovertebral, que pot fixar la medul\u00b7la espinal al canal vertebral.<\/p>\r\n<p><strong>Tipus III.<\/strong> Descens de les am\u00edgdales cerebel\u00b7loses amb encefalocele occipital i anomalies cerebrals.<\/p>\r\n<p><strong>Tipus IV.<\/strong> Descens de les am\u00edgdales cerebel\u00b7loses amb apl\u00e0sia o hipopl\u00e0sia del cerebel associada amb apl\u00e0sia de la tenda del cerebel.<\/p>\r\n<p>Tipus &#8220;0&#8221;. Actualment s&#8217;ha comentat l&#8217;exist\u00e8ncia de casos amb la cl\u00ednica pr\u00f2pia del SACH.I per\u00f2 sense descens de les am\u00edgdales cerebel\u00b7loses.<\/p>\r\n<p><strong>Tipus &#8220;1,5&#8221;.<\/strong> Recentment s&#8217;ha descrit la s\u00edndrome d&#8217;Arnold-Chiari &#8220;1,5&#8221; amb descens de les am\u00edgdales cerebel\u00b7loses i herniaci\u00f3 del tronc cerebral al forat occipital.<\/p>\r\n<hr \/>\r\n<h2><strong>Causa del descens de les am\u00edgdales cerebel\u00b7loses: Teories<\/strong><\/h2>\r\n<p>El descens de les am\u00edgdales cerebel\u00b7loses (DAC) pot produir-se com a resultat de la tracci\u00f3 que exerceixen sobre la medul\u00b7la espinal malformacions associades a algunes formes de s\u00edndrome d&#8217;Arnold-Chiari; excepte en el Tipus I, on el descens de les am\u00edgdales cerebel\u00b7loses \u00e9s l&#8217;\u00fanica alteraci\u00f3 morfol\u00f2gica \u2014en aquest cas hi ha diverses teories\u2014:<\/p>\r\n<p><strong>&#8211; Teories convencionals:<\/strong><\/p>\r\n<ul>\r\n<li style=\"font-size: 16px; font-weight: 300; text-align: justify;\"><strong>Hidrodin\u00e0mica:<\/strong> el descens de les am\u00edgdales cerebel\u00b7loses \u00e9s conseq\u00fc\u00e8ncia d&#8217;una anomalia de la circulaci\u00f3 del LCR.<\/li>\r\n<\/ul>\r\n<p>&nbsp;<\/p>\r\n<ul>\r\n<li style=\"font-size: 16px; font-weight: 300; text-align: justify;\"><strong>Malformativa:<\/strong> La teoria de la fossa cranial petita considera que aquesta malformaci\u00f3 indueix el cerebel a herniar-se cap al canal vertebral.<\/li>\r\n<\/ul>\r\n<p><strong>&#8211; Teoria de la tracci\u00f3 medul\u00b7lar, segons el Filum System <sup>\u00ae<\/sup>:<\/strong><\/p>\r\n<p>La teoria del Dr. Miguel B. Royo Salvador considera el descens de les am\u00edgdales cerebel\u00b7loses en una S\u00edndrome d&#8217;Arnold Chiari I com a resultat d&#8217;una tracci\u00f3 anormal de la medul\u00b7la espinal, deguda a un lligament del Filum Terminale an\u00f2mal i excessivament tens (no evidenciable en les exploracions complement\u00e0ries).<\/p>\r\n<div align=\"center\"><img decoding=\"async\" class=\"aligncenter size-full wp-image-7932 img-responsive\" src=\"https:\/\/institutchiaribcn.com\/wp-content\/uploads\/2019\/01\/Resonancia-magnetica-DAC.jpg\" alt=\"\" \/><\/div>\r\n<p><em>Figura 2.- Resson\u00e0ncia Magn\u00e8tica (RM) d&#8217;una pacient als 8 i 20 mesos, en la qual es pot observar un DAC sorgit entre les dues RM. Huang P. &#8220;Adquired&#8221; Chiari I malformation. J. Neurosurg 1994. Indicant que a m\u00e9s d&#8217;un component gen\u00e8tic i hereditari hi ha un factor adquirit.<br \/><\/em><\/p>\r\n<hr \/>\r\n<h2><strong>Factors de risc de la S\u00edndrome d&#8217;Arnold Chiari I<\/strong><\/h2>\r\n<p>Els factors de risc amb m\u00e9s influ\u00e8ncia en el desenvolupament de la S\u00edndrome d&#8217;Arnold Chiari I s\u00f3n els seg\u00fcents:<\/p>\r\n<ul>\r\n<li style=\"font-size: 16px; font-weight: 300; text-align: justify;\"><strong>Antecedents familiars<\/strong>: La tracci\u00f3 caudal de tot el sistema nervi\u00f3s, produ\u00efda per un Filum terminale excessivament tens, que definim com a Malaltia del Filum i que causa el mecanisme de descens de les am\u00edgdales cerebel\u00b7loses. Es tracta d&#8217;una patologia de tipus cong\u00e8nit que es pot transmetre entre familiars.<\/li>\r\n<\/ul>\r\n<p>&nbsp;<\/p>\r\n<ul>\r\n<li style=\"font-size: 16px; font-weight: 300; text-align: justify;\"><strong>Augment sobtat de la tracci\u00f3 medul\u00b7lar:<\/strong> S&#8217;ha observat que despr\u00e9s d&#8217;un accident, caiguda o trauma de la columna vertebral \u2014amb una medul\u00b7la espinal que ja pateix cong\u00e8nitament la Malaltia del Filum\u2014 la tracci\u00f3 medul\u00b7lar pot augmentar. En aquestes circumst\u00e0ncies de major tracci\u00f3 medul\u00b7lar caudal, es poden observar empitjoraments del descens de les am\u00edgdales cerebel\u00b7loses o de la compressi\u00f3 al foramen magnum, a trav\u00e9s dels s\u00edmptomes. L&#8217;accident en aquests casos no \u00e9s la causa del descens amigdalar, sin\u00f3 que desencadena un empitjorament sobtat del mecanisme de tracci\u00f3 preexistent, tant anat\u00f2micament com a nivell dels trastorns cl\u00ednics.<\/li>\r\n<\/ul>\r\n<hr \/>\r\n<h2><strong>Complicacions de la S\u00edndrome d&#8217;Arnold Chiari I<\/strong><\/h2>\r\n<p>Les complicacions de l&#8217;ect\u00f2pia de les am\u00edgdales cerebel\u00b7loses poden dependre del grau de tracci\u00f3 caudal o de la compressi\u00f3 associada al forat occipital. Aquesta \u00faltima \u00e9s determinada pel conflicte entre la tracci\u00f3 de la medul\u00b7la i del tronc cerebral i l&#8217;espai disponible al forat.<\/p>\r\n<ul>\r\n<li style=\"font-size: 16px; font-weight: 300; text-align: justify;\"><strong>Empitjorament de la qualitat de vida:<\/strong> a l&#8217;Arnold Chiari I les cefalees, els v\u00e8rtigs, els dolors a la columna o a les extremitats, les par\u00e8sies, les alteracions de la degluci\u00f3 o de la sensibilitat, les alteracions cognitives, les alteracions visuals o de la marxa, poden arribar a ser cr\u00f2niques, augmentant en intensitat i deteriorant cada vegada m\u00e9s l&#8217;estat del malalt, limitant la seva activitat normal.<\/li>\r\n<li style=\"font-size: 16px; font-weight: 300; text-align: justify;\"><strong>Dolor cr\u00f2nic:<\/strong> Els pacients poden arribar a necessitar el tractament d&#8217;una Unitat del Dolor, perqu\u00e8 els medicaments antiinflamatoris o analg\u00e8sics de primera elecci\u00f3 poden arribar a no ser suficients per suportar els s\u00edmptomes de dolor i les crisis de cefalea caracter\u00edstiques de la malaltia.<\/li>\r\n<li style=\"font-size: 16px; font-weight: 300; text-align: justify;\"><strong>Mort sobtada:<\/strong> a causa del control de les funcions cardiorespirat\u00f2ries de la zona del tronc cerebral, on s&#8217;ubiquen les am\u00edgdales cerebel\u00b7loses i es desenvolupa la compressi\u00f3, els trastorns respiratoris durant el son poden constituir un aspecte de la patologia, podent expressar-se en apnees, fallades respirat\u00f2ries o fins i tot en la mort sobtada del pacient. D&#8217;aqu\u00ed la import\u00e0ncia d&#8217;un diagn\u00f2stic i d&#8217;un tractament preco\u00e7.<\/li>\r\n<\/ul>\r\n<hr \/>\r\n<h2><strong>Tractaments de la S\u00edndrome d&#8217;Arnold Chiari I<\/strong><\/h2>\r\n<p>El tractament convencionalment acceptat per a la S\u00edndrome d&#8217;Arnold Chiari I \u00e9s neuroquir\u00fargic.<\/p>\r\n<p>Actualment la craniectomia o descompressi\u00f3 suboccipital \u00e9s el tractament est\u00e0ndard que es realitza a la majoria dels centres del m\u00f3n per a aquest diagn\u00f2stic, amb o sense Siringomielia. Sol indicar-se especialment per a casos simptom\u00e0tics, ja que provoca m\u00e9s morbiditat i mortalitat que l&#8217;evoluci\u00f3 natural de la mateixa patologia.<\/p>\r\n<p>Des de 1993, en canvi, amb la publicaci\u00f3 de la tesi doctoral del Dr. Royo Salvador, que relaciona la tracci\u00f3 caudal de tot el sistema nervi\u00f3s pel filum terminale com a causa de l&#8217;ect\u00f2pia de les am\u00edgdales cerebel\u00b7loses \u2014entre altres malalties\u2014, s&#8217;ha dissenyat un nou tractament, que en aquest cas \u00e9s etiol\u00f2gic o quant a la causa, ja que en seccionar quir\u00fargicament el filum terminale s&#8217;elimina la for\u00e7a de tracci\u00f3 medul\u00b7lar caudal responsable del mecanisme patol\u00f2gic.<\/p>\r\n<p>La nostra t\u00e8cnica de Secci\u00f3 del Filum terminale (SFT) \u00e9s m\u00ednimament invasiva i sol indicar-se en tots els casos, simptom\u00e0tics o no simptom\u00e0tics, i com m\u00e9s aviat millor, ja que t\u00e9 riscos m\u00ednims i molt inferiors als de la patologia en si, a m\u00e9s d&#8217;aturar-ne l&#8217;evoluci\u00f3.<\/p>\r\n<div class=\"row\">\r\n<div align=\"center\">\r\n<h3><strong>Secci\u00f3 del Filum Terminale (SFT) m\u00ednimament invasiva segons el Filum System\u00ae:<\/strong><\/h3>\r\n<\/div>\r\n<p>&nbsp;<\/p>\r\n<div class=\"col-md-6\">\r\n<div class=\"boxAdvantages barAdvantages\">\r\n<div align=\"center\">\r\n<h3><strong>Avantatges<\/strong><\/h3>\r\n<\/div>\r\n<p>&nbsp;<\/p>\r\n<p style=\"text-align: justify; padding-left: 30px;\">1. Elimina la causa de l&#8217;Arnold Chiari I i de diverses patologies associades.<\/p>\r\n<p>&nbsp;<\/p>\r\n<p style=\"text-align: justify; padding-left: 30px;\">2. Elimina la compressi\u00f3 al foramen magnum, i amb ella el risc de mort sobtada.<\/p>\r\n<p>&nbsp;<\/p>\r\n<p style=\"text-align: justify; padding-left: 30px;\">3. La seva aplicaci\u00f3 suposa el 0% de mortalitat, sense seq\u00fceles en m\u00e9s de 1.500 casos operats amb el nostre m\u00e8tode Filum System\u00ae.<\/p>\r\n<p>&nbsp;<\/p>\r\n<p style=\"text-align: justify; padding-left: 30px;\">4. Amb la t\u00e8cnica m\u00ednimament invasiva, el temps quir\u00fargic \u00e9s de 45 minuts. Poques hores d&#8217;ingr\u00e9s. Anest\u00e8sia local. Postoperatori curt i sense limitacions.<\/p>\r\n<p>&nbsp;<\/p>\r\n<p style=\"text-align: justify; padding-left: 30px;\">5. Millora els s\u00edmptomes i atura l&#8217;evoluci\u00f3 del descens de les am\u00edgdales cerebel\u00b7loses a trav\u00e9s del forat occipital.<\/p>\r\n<p>&nbsp;<\/p>\r\n<p style=\"text-align: justify; padding-left: 30px;\">6. Evita la hidrocef\u00e0lia per l&#8217;impacte de les am\u00edgdales cerebel\u00b7loses.<\/p>\r\n<p>&nbsp;<\/p>\r\n<p style=\"text-align: justify; padding-left: 30px;\">7. Millora la circulaci\u00f3 sangu\u00ednia a tot el SN i amb aix\u00f2 les facultats cognitives que poden estar afectades per la tracci\u00f3 medul\u00b7lar.<\/p>\r\n<\/div>\r\n<p>&nbsp;<\/p>\r\n<\/div>\r\n<p>&nbsp;<\/p>\r\n<div class=\"col-md-6\">\r\n<div class=\"boxDisadvantages barDisadvantages\">\r\n<div align=\"center\">\r\n<h3><strong>Desavantatges<\/strong><\/h3>\r\n<\/div>\r\n<p>&nbsp;<\/p>\r\n<p style=\"text-align: justify; padding-left: 30px;\">1. M\u00ednima ferida al sacre, amb les possibles complicacions d&#8217;hematoma o infecci\u00f3 de la ferida quir\u00fargica.<\/p>\r\n<p>&nbsp;<\/p>\r\n<p style=\"text-align: justify; padding-left: 30px;\">2. En cas d&#8217;espasticitat, de vegades s&#8217;interpreta err\u00f2niament la seva millora com a disminuci\u00f3 de la for\u00e7a.<\/p>\r\n<p>&nbsp;<\/p>\r\n<p style=\"text-align: justify; padding-left: 30px;\">3. En el cas d&#8217;alteracions de les sensacions t\u00e0ctils i la recepci\u00f3 del dolor, de vegades la seva millora s&#8217;interpreta err\u00f2niament com a inconvenients.<\/p>\r\n<p>&nbsp;<\/p>\r\n<p style=\"text-align: justify; padding-left: 30px;\">4. En augmentar el reg cerebral, augmenta l&#8217;activitat cerebral i es poden observar alteracions an\u00edmiques durant el primer per\u00edode postoperatori.<\/p>\r\n<\/div>\r\n<p>&nbsp;<\/p>\r\n<\/div>\r\n<p>&nbsp;<\/p>\r\n<\/div>\r\n<p>&nbsp;<\/p>\r\n<div align=\"center\">\r\n<h3><strong>Craniectomia suboccipital:<\/strong><\/h3>\r\n<h3>(Descompressi\u00f3 del foramen magnum o forat occipital)<\/h3>\r\n<\/div>\r\n<p>&nbsp;<\/p>\r\n<div class=\"row\">\r\n<div class=\"col-md-6\">\r\n<div class=\"boxAdvantages barAdvantages\">\r\n<div align=\"center\">\r\n<h3><strong>Avantatges<\/strong><\/h3>\r\n<\/div>\r\n<p>&nbsp;<\/p>\r\n<p style=\"text-align: justify; padding-left: 30px;\">1. Elimina el risc de la mort sobtada.<\/p>\r\n<p>&nbsp;<\/p>\r\n<p style=\"text-align: justify; padding-left: 30px;\">2. Alguns pacients milloren cl\u00ednicament.<\/p>\r\n<\/div>\r\n<p>&nbsp;<\/p>\r\n<\/div>\r\n<p>&nbsp;<\/p>\r\n<div class=\"col-md-6\">\r\n<div class=\"boxDisadvantages barDisadvantages\">\r\n<div align=\"center\">\r\n<h3><strong>Desavantatges<\/strong><\/h3>\r\n<\/div>\r\n<p>&nbsp;<\/p>\r\n<p style=\"text-align: justify; padding-left: 30px;\">1. No elimina la causa.<\/p>\r\n<p>&nbsp;<\/p>\r\n<p style=\"text-align: justify; padding-left: 30px;\">2. Del 0,7 al 12% de mortalitat, amb un percentatge m\u00e9s gran de risc de la intervenci\u00f3 que el de mort sobtada de la patologia.<\/p>\r\n<p>&nbsp;<\/p>\r\n<p style=\"text-align: justify; padding-left: 30px;\">3. Agressiva, mutilant i amb seq\u00fceles.<\/p>\r\n<p>&nbsp;<\/p>\r\n<p style=\"text-align: justify; padding-left: 30px;\">4. Millora poc la condici\u00f3 del malalt, i per un temps limitat (que s&#8217;estima en 10 anys de mitjana).<\/p>\r\n<p>&nbsp;<\/p>\r\n<p style=\"text-align: justify; padding-left: 30px;\">5. Depenent de la localitzaci\u00f3 de la lesi\u00f3, la mateixa intervenci\u00f3 pot causar d\u00e8ficit neurol\u00f2gic: Hemipar\u00e8sia (par\u00e0lisi de l&#8217;hemicos) de 0,5 a 2,1%. Alteraci\u00f3 del camp visual de 0,2 a 1,4%. Trastorn del llenguatge de 0,4 a 1%. D\u00e8ficit sensitiu de 0,3 a 1%. Inestabilitat (dificultat per caminar) del 10 al 30%.<\/p>\r\n<p>&nbsp;<\/p>\r\n<p style=\"text-align: justify; padding-left: 30px;\">6. Hemorr\u00e0gia intracerebral postoperat\u00f2ria, del llit quir\u00fargic, epidural o intraparenquimatosa, causant d\u00e8ficit neurol\u00f2gic o empitjorament d&#8217;un d\u00e8ficit preexistent de 0,1 a 5%.<\/p>\r\n<p>&nbsp;<\/p>\r\n<p style=\"text-align: justify; padding-left: 30px;\">7. Infart-edema, variable depenent del proc\u00e9s i la situaci\u00f3, fins al 5%.<\/p>\r\n<p>&nbsp;<\/p>\r\n<p style=\"text-align: justify; padding-left: 30px;\">8. Infecci\u00f3 superficial de 0,1 a 6,8% profunda o cerebral, amb formaci\u00f3 d&#8217;absc\u00e9s cerebral, meningitis as\u00e8ptica-s\u00e8ptica.<\/p>\r\n<p>&nbsp;<\/p>\r\n<p style=\"text-align: justify; padding-left: 30px;\">9. Alteraci\u00f3 hemodin\u00e0mica per la manipulaci\u00f3 de lesions del tronc cerebral.<\/p>\r\n<p>&nbsp;<\/p>\r\n<p style=\"text-align: justify; padding-left: 30px;\">10. Emb\u00f2lia gasosa (malalts en posici\u00f3 quir\u00fargica de sedestaci\u00f3).<\/p>\r\n<p>&nbsp;<\/p>\r\n<p style=\"text-align: justify; padding-left: 30px;\">11. F\u00edstula o fuita de l\u00edquid cefaloraquidi del 3 al 14% (f\u00edstula de LCR).<\/p>\r\n<p>&nbsp;<\/p>\r\n<p style=\"text-align: justify; padding-left: 30px;\">12. Hidrocef\u00e0lia postoperat\u00f2ria.<\/p>\r\n<p>&nbsp;<\/p>\r\n<p style=\"text-align: justify; padding-left: 30px;\">13. Pneumoenc\u00e8fal.<\/p>\r\n<p>&nbsp;<\/p>\r\n<p style=\"text-align: justify; padding-left: 30px;\">14. Tetrapar\u00e8sia (p\u00e8rdua de for\u00e7a a les 4 extremitats) per la posici\u00f3 quir\u00fargica, de forma casual.<\/p>\r\n<\/div>\r\n<p>&nbsp;<\/p>\r\n<\/div>\r\n<p>&nbsp;<\/p>\r\n<\/div>\r\n<p>&nbsp;<\/p>\r\n<div align=\"center\"><a href=\"https:\/\/institutchiaribcn.com\/wp-content\/uploads\/2017\/05\/Mortalidad-CSO-y-SFT.png\"><img decoding=\"async\" class=\"img-rounded img-responsive\" src=\"https:\/\/institutchiaribcn.com\/wp-content\/uploads\/2017\/05\/Mortalidad-CSO-y-SFT.png\" alt=\"\" width=\"auto\" height=\"auto\" \/><\/a><br \/><a href=\"https:\/\/institutchiaribcn.com\/wp-content\/uploads\/2015\/05\/Crainectomia-desventajas.png\"><img decoding=\"async\" class=\"img-rounded img-responsive\" src=\"https:\/\/institutchiaribcn.com\/wp-content\/uploads\/2015\/05\/Crainectomia-desventajas.png\" alt=\"\" width=\"662\" height=\"auto\" \/><\/a><\/div>\r\n<p>&nbsp;<\/p>\r\n<div align=\"center\">\u00a0<\/div>\r\n<p>&nbsp;<\/p>\r\n<h3 style=\"text-align: center;\">A causa de les complicacions i la mortalitat de la Craniectomia suboccipital, m\u00e9s gran que l&#8217;evoluci\u00f3 espont\u00e0nia de la s\u00edndrome d&#8217;Arnold Chiari I, la considerem contraindicada.<\/h3>\r\n<p>&nbsp;<\/p>\r\n<div align=\"center\">\u00a0<\/div>\r\n<p>&nbsp;<\/p>\r\n<div align=\"center\">\u00a0<\/div>\r\n<hr \/>\r\n<h2><strong>Resultats de la Secci\u00f3 del Filum Terminale<\/strong><\/h2>\r\n<p>Amb el m\u00e8tode del Filum System\u00ae ja s&#8217;han operat m\u00e9s de 1500 pacients amb S\u00edndrome d&#8217;Arnold Chiari I, amb o sense Siringomielia idiop\u00e0tica i\/o Escoliosi idiop\u00e0tica.<\/p>\r\n<p>El prop\u00f2sit de la intervenci\u00f3 quir\u00fargica \u00e9s aturar l&#8217;evoluci\u00f3 de la malaltia i que ni l&#8217;ect\u00f2pia ni les lesions augmentin ulteriorment. No obstant aix\u00f2, en alguns casos s&#8217;han aconseguit millores notables de l&#8217;estat cl\u00ednic, i fins i tot amb l&#8217;ascens de les am\u00edgdales cerebel\u00b7loses.<\/p>\r\n<p>Exemples:<\/p>\r\n<div class=\"col-md-9\">Cas N\u00ba 11435<\/div>\r\n<p><img decoding=\"async\" class=\"aligncenter img-responsive\" src=\"https:\/\/institutchiaribcn.com\/wp-content\/uploads\/2023\/03\/chiari2-new.jpg\" alt=\"\" width=\"800\" \/><\/p>\r\n<div>\u00a0<\/div>\r\n<hr \/>\r\n<div class=\"col-md-9\">Cas N\u00ba 12535<\/div>\r\n<p><img decoding=\"async\" class=\"aligncenter img-responsive\" src=\"https:\/\/institutchiaribcn.com\/wp-content\/uploads\/2023\/03\/chiari1-new.jpg\" alt=\"\" width=\"800\" \/><\/p>\r\n<div>\u00a0<\/div>\r\n<hr \/>\r\n<div class=\"row\">\r\n<div class=\"col-md-9\">Cas N\u00ba 16453<\/div>\r\n<p>&nbsp;<\/p>\r\n<\/div>\r\n<p>&nbsp;<\/p>\r\n<div class=\"row\">\r\n<div class=\"col-md-4\">\r\n<div align=\"center\">\r\n<div align=\"center\"><img decoding=\"async\" class=\"img-rounded wp-image-1582 size-medium\" src=\"https:\/\/institutchiaribcn.com\/wp-content\/uploads\/2015\/05\/evolucion_seccion_filum_terminale_2008_caso-16453-252x300.jpg\" alt=\"arnold chiari - evolucion_seccion_filum_terminale_2008_caso-16453\" width=\"252\" height=\"300\" \/><\/div>\r\n<p>&nbsp;<\/p>\r\n<div align=\"center\">2008<\/div>\r\n<p>&nbsp;<\/p>\r\n<\/div>\r\n<p>&nbsp;<\/p>\r\n<\/div>\r\n<p>&nbsp;<\/p>\r\n<div class=\"col-md-1\">\u00a0<\/div>\r\n<p>&nbsp;<\/p>\r\n<div class=\"col-md-4\">\r\n<div align=\"center\">\r\n<div align=\"center\"><img loading=\"lazy\" decoding=\"async\" class=\"img-rounded size-medium wp-image-1581\" src=\"https:\/\/institutchiaribcn.com\/wp-content\/uploads\/2015\/05\/evolucion_seccion_filum_terminale_2010_caso-16453.jpg-258x300.jpg\" alt=\"arnold chiari - 2010\" width=\"252\" height=\"300\" \/><\/div>\r\n<p>&nbsp;<\/p>\r\n<div align=\"center\">2010<\/div>\r\n<p>&nbsp;<\/p>\r\n<\/div>\r\n<p>&nbsp;<\/p>\r\n<\/div>\r\n<p>&nbsp;<\/p>\r\n<\/div>\r\n<p>&nbsp;<\/p>\r\n<div class=\"row\">\r\n<div class=\"col-md-9\">Cas N\u00ba 14183<\/div>\r\n<p>&nbsp;<\/p>\r\n<\/div>\r\n<p>&nbsp;<\/p>\r\n<div class=\"row\">\r\n<div class=\"col-md-4\">\r\n<div align=\"center\">\r\n<div align=\"center\"><img loading=\"lazy\" decoding=\"async\" class=\"img-rounded size-full wp-image-1610\" src=\"https:\/\/institutchiaribcn.com\/wp-content\/uploads\/2015\/05\/evolucion_seccion_filum_terminale_2011_caso-14183.jpg\" alt=\"arnold chiari - 2011\" width=\"252\" height=\"237\" \/><\/div>\r\n<p>&nbsp;<\/p>\r\n<div align=\"center\">2011<\/div>\r\n<p>&nbsp;<\/p>\r\n<\/div>\r\n<p>&nbsp;<\/p>\r\n<\/div>\r\n<p>&nbsp;<\/p>\r\n<div class=\"col-md-1\">\u00a0<\/div>\r\n<p>&nbsp;<\/p>\r\n<div class=\"col-md-4\">\r\n<div align=\"center\">\r\n<div align=\"center\"><img loading=\"lazy\" decoding=\"async\" class=\"img-rounded size-full wp-image-1609\" src=\"https:\/\/institutchiaribcn.com\/wp-content\/uploads\/2015\/05\/evolucion_seccion_filum_terminale_2012_caso-14183.jpg\" alt=\"arnold chiari - 2012\" width=\"252\" height=\"237\" \/><\/div>\r\n<p>&nbsp;<\/p>\r\n<div align=\"center\">2012<\/div>\r\n<p>&nbsp;<\/p>\r\n<\/div>\r\n<p>&nbsp;<\/p>\r\n<\/div>\r\n<p>&nbsp;<\/p>\r\n<\/div>\r\n<p>&nbsp;<\/p>\r\n<div class=\"row\">\r\n<div class=\"col-md-9\">Cas N\u00ba 15704<\/div>\r\n<p>&nbsp;<\/p>\r\n<\/div>\r\n<p>&nbsp;<\/p>\r\n<div class=\"row\">\r\n<div class=\"col-md-4\">\r\n<div align=\"center\">\r\n<div align=\"center\"><img loading=\"lazy\" decoding=\"async\" class=\"img-rounded size-full wp-image-1607\" src=\"https:\/\/institutchiaribcn.com\/wp-content\/uploads\/2015\/05\/evolucion_seccion_filum_terminale_2010_caso-15704.jpg\" alt=\"arnold chiari - 2010\" width=\"252\" height=\"236\" \/><\/div>\r\n<p>&nbsp;<\/p>\r\n<div align=\"center\">2010<\/div>\r\n<p>&nbsp;<\/p>\r\n<\/div>\r\n<p>&nbsp;<\/p>\r\n<\/div>\r\n<p>&nbsp;<\/p>\r\n<div class=\"col-md-1\">\u00a0<\/div>\r\n<p>&nbsp;<\/p>\r\n<div class=\"col-md-4\">\r\n<div align=\"center\">\r\n<div align=\"center\"><img loading=\"lazy\" decoding=\"async\" class=\"img-rounded size-full wp-image-1608\" src=\"https:\/\/institutchiaribcn.com\/wp-content\/uploads\/2015\/05\/evolucion_seccion_filum_terminale_2011_caso-15704.jpg\" alt=\"arnold chiari - 2011\" width=\"252\" height=\"235\" \/><\/div>\r\n<p>&nbsp;<\/p>\r\n<div align=\"center\">2011<\/div>\r\n<p>&nbsp;<\/p>\r\n<\/div>\r\n<p>&nbsp;<\/p>\r\n<\/div>\r\n<p>&nbsp;<\/p>\r\n<\/div>\r\n<hr \/>\r\n<h2><strong>BIBLIOGRAFIA<\/strong><\/h2>\r\n<p>&nbsp;<\/p>\r\n<ol>\r\n<li style=\"font-size: 16px; font-weight: 300; text-align: justify;\">Royo-Salvador M.B., Fiallos-Rivera M.V., Salca H.C.;,Oll\u00e9-Fortuny, G. (2020), <a class=\"external text\" href=\"https:\/\/link.springer.com\/epdf\/10.1186\/s12883-020-01743-y\" target=\"_blank\" rel=\"noopener noreferrer\">The Filum disease and the Neuro-Craniovertebral syndrome: definition, clinical picture and imaging features<\/a>, 20:175, BMC Neurology<\/li>\r\n<li style=\"font-size: 16px; font-weight: 300; text-align: justify;\">Royo-Salvador M.B. (1996), <a href=\"https:\/\/institutchiaribcn.com\/pdf\/publicaciones\/dr-royo\/Siringomielia-escoliosis-malformacion-Arnold_Chiari-idiopatica.pdf\" target=\"_blank\" rel=\"noopener noreferrer\"><strong>Siringomi\u00e8lia<\/strong>, <strong>escoliosi<\/strong> i malformaci\u00f3 d&#8217;<strong>Arnold-Chiari<\/strong> idiop\u00e0tiques, etiologia comuna (PDF).<\/a> REV NEUROL (Barc); 24 (132): 937-959.<\/li>\r\n<li style=\"font-size: 16px; font-weight: 300; text-align: justify;\">Royo-Salvador M.B. (1996), <a href=\"https:\/\/institutchiaribcn.com\/pdf\/publicaciones\/dr-royo\/platibasia-impresion-basilar-retroceso-odontoideo.pdf\" target=\"_blank\" rel=\"noopener noreferrer\"><strong>Platib\u00e0sia<\/strong>, impressi\u00f3 basilar, retroc\u00e9s odontoide i kinking del tronc cerebral, etiologia comuna amb la <strong>siringomi\u00e8lia<\/strong>, <strong>escoliosi<\/strong> i <strong>malformaci\u00f3 d&#8217;Arnold-Chiari<\/strong> idiop\u00e0tiques (PDF).<\/a> REV NEUROL (Barc); 24 (134): 1241-1250<\/li>\r\n<li style=\"font-size: 16px; font-weight: 300; text-align: justify;\">Royo-Salvador M.B. (1997), <a href=\"https:\/\/institutchiaribcn.com\/pdf\/publicaciones\/dr-royo\/Nuevo-tratamiento-sirignomielia-escoliosis-malformacion-Arnold_Chiari.pdf\" target=\"_blank\" rel=\"noopener noreferrer\">Nou tractament quir\u00fargic per a la <strong>siringomi\u00e8lia<\/strong>, l&#8217;<strong>escoliosi<\/strong>, la <strong>malformaci\u00f3 d&#8217;Arnold-Chiari<\/strong>, el kinking del tronc cerebral, el retroc\u00e9s odontoide, la impressi\u00f3 basilar i la platib\u00e0sia idiop\u00e0tiques (PDF).<\/a> REV NEUROL; 25 (140): 523-530<\/li>\r\n<li style=\"font-size: 16px; font-weight: 300; text-align: justify;\">Royo-Salvador M.B., Sol\u00e9-Llenas J., Dom\u00e9nech J.M., Gonz\u00e1lez-Adrio R. (2005) <a href=\"https:\/\/institutchiaribcn.com\/pdf\/publicaciones\/dr-royo\/results-filum-in-20-patients.pdf\" target=\"_blank\" rel=\"noopener noreferrer\">&#8220;Results of the section of the <strong>filum terminale<\/strong> in 20 patients with <strong>syringomyelia<\/strong>, scoliosis and <strong>Chiari malformation<\/strong>&#8220;.(PDF).<\/a> Acta Neurochir (Wien) 147: 515\u2013523.<\/li>\r\n<li style=\"font-size: 16px; font-weight: 300; text-align: justify;\">Royo-Salvador M.B. (1992), <a href=\"https:\/\/institutchiaribcn.com\/pdf\/publicaciones\/dr-royo\/tesis_doctoral-Aportacion-etiologia-Siringomielia.pdf\" target=\"_blank\" rel=\"noopener noreferrer\">&#8220;Aportaci\u00f3 a l&#8217;etiologia de la <strong>siringomi\u00e8lia<\/strong>&#8220;, Tesi doctoral (PDF).<\/a> Universitat Aut\u00f2noma de Barcelona.<\/li>\r\n<li style=\"font-size: 16px; font-weight: 300; text-align: justify;\">Royo-Salvador M.B. (2014), <a href=\"https:\/\/institutchiaribcn.com\/commons\/pdf\/publicaciones\/dr-royo\/filum-system-bibliography.pdf\" target=\"_blank\" rel=\"noopener noreferrer\">&#8220;Filum System<sup>\u00ae<\/sup> Bibliography&#8221; (PDF).<\/a><\/li>\r\n<li style=\"font-size: 16px; font-weight: 300; text-align: justify;\">Royo-Salvador M.B. (2014), <a href=\"https:\/\/institutchiaribcn.com\/filum-system-guia-breve\/\" target=\"_blank\" rel=\"noopener noreferrer\">&#8220;Filum System<sup>\u00ae<\/sup> Guia Breu&#8221;.<\/a><\/li>\r\n<li style=\"font-size: 16px; font-weight: 300; text-align: justify;\">Royo-Salvador M.B., Fiallos-Rivera M. and Salca H. (November 20th 2019). Caudal Traction as a Pathogenetic Mechanism of Chiari Malformation Type I [Online First], IntechOpen, DOI: 10.5772\/intechopen.90044. Available from: <a href=\"https:\/\/www.intechopen.com\/online-first\/caudal-traction-as-a-pathogenetic-mechanism-of-chiari-malformation-type-i\" rel=\"noopener noreferrer\">https:\/\/www.intechopen.com\/online-first\/caudal-traction-as-a-pathogenetic-mechanism-of-chiari-malformation-type-i<\/a><\/li>\r\n<\/ol>\r\n<p><button class=\"btn-full btn btn-primary fade-hover\" type=\"button\" data-toggle=\"collapse\" data-target=\"#collapseExample\" aria-expanded=\"false\" aria-controls=\"collapseExample\" aria-label=\"Left Align\">Veure m\u00e9s<\/button><\/p>\r\n<div id=\"collapseExample\" class=\"collapse\">\r\n<div class=\"well\"><hr \/>\r\n<h2><strong>S\u00edndrome d&#8217;Arnold Chiari I<\/strong><\/h2>\r\n<p><strong>Descrit:<\/strong> El 1883 pel cirurgi\u00e0 anatomista John Cleland (1835-1925) de Pertshire, Esc\u00f2cia. Va descriure l&#8217;elongaci\u00f3 del vermis cerebel\u00b7l\u00f3s, el descens del cerebel i del IV ventricle en un nen amb hidrocef\u00e0lia, encefalocele, espina b\u00edfida i mielosquisi. El 1891 i 1896 Hans Chiari va aportar nous casos i la seva classificaci\u00f3. El 1894 Julius Arnold va contribuir a la seva difusi\u00f3.<\/p>\r\n<p><strong>Nominat:<\/strong> Per Schwalbe i Gredig el 1907, com a &#8220;malformaci\u00f3 d&#8217;Arnold-Chiari&#8221;. La nomenclatura oficial actual en el Codi de classificaci\u00f3 de les malalties de l&#8217;OMS (International Statistical Classification of Diseases and Related Health Problems, 10th Revision (c) Geneva, OMS, 1992), consta per a aquesta malaltia amb la terminologia de &#8220;S\u00edndrome o malaltia d&#8217;Arnold-Chiari I&#8221; (Q07.0, CIE-10).<\/p>\r\n<p><strong>Incid\u00e8ncia:<\/strong> Un cas de cada mil nascuts vius; altres autors revelen una mica menys de l&#8217;u per cent de la poblaci\u00f3. En tots dos casos s\u00f3n xifres amb criteris actuals molt restrictius, amb un DAC &gt; 3 o 5 mm.<\/p>\r\n<hr \/>\r\n<h2><strong>Malaltia del Filum<\/strong><\/h2>\r\n<p>Despr\u00e9s dels estudis del Dr. Royo Salvador (1992) amb la seva tesi doctoral, va passar de teoria a fet provat considerar que diverses malalties de causa desconeguda, com: s\u00edndrome d&#8217;Arnold Chiari I, Siringomi\u00e8lia i Escoliosi idiop\u00e0tiques, Platib\u00e0sia, Impressi\u00f3 Basilar, Retroc\u00e9s odontoide, Angulaci\u00f3 del tronc cerebral, formen part \u2014compartint causa\u2014: la tracci\u00f3 de la medul\u00b7la espinal i de tot el sistema nervi\u00f3s, d&#8217;un nou concepte de patologia; la Malaltia del Filum.<\/p>\r\n<p>La for\u00e7a de tracci\u00f3 de tot el sistema nervi\u00f3s a la Malaltia del Filum es presenta en tots els embrions humans, de manera que en major o menor mesura en pateixen les conseq\u00fc\u00e8ncies i es manifesten de formes molt diverses i intensitats.<\/p>\r\n<p>A la Malaltia del Filum hi estan involucrades, per la seva causa, altres malalties com les h\u00e8rnies discals vertebrals, alguns s\u00edndromes d&#8217;insufici\u00e8ncia vascular cerebral, s\u00edndromes de la faceta articular i de Baastrup, fibromi\u00e0lgia, fatiga cr\u00f2nica, enuresi nocturna, incontin\u00e8ncia urin\u00e0ria i parapar\u00e8sies acusades.<\/p>\r\n<p>Per precisar el diagn\u00f2stic, orientar el tractament i el seguiment de la Malaltia del Filum s&#8217;ha confeccionat un m\u00e8tode sanitari: <a href=\"https:\/\/institutchiaribcn.com\/ca\/presentacio-filum-system\/\">el Filum System\u00ae.<\/a><\/p>\r\n<\/div>\r\n<p>&nbsp;<\/p>\r\n<\/div>\r\n\r\n<p>&nbsp;<\/p>\r\n","protected":false},"featured_media":1313,"template":"","class_list":["post-15058","enfermedades","type-enfermedades","status-publish","has-post-thumbnail","hentry"],"yoast_head":"<!-- This site is optimized with the Yoast SEO plugin v27.1.1 - https:\/\/yoast.com\/product\/yoast-seo-wordpress\/ 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