{"id":75965,"date":"2025-05-30T00:00:00","date_gmt":"2025-05-29T22:00:00","guid":{"rendered":"https:\/\/dev.institutchiaribcn.com\/comunicacion\/nou-article-cientific-sobre-la-sindrome-neuro-cranio-vertebral-associada-a-la-sindrome-dehlers-danlos\/"},"modified":"2026-03-17T12:51:37","modified_gmt":"2026-03-17T11:51:37","slug":"nou-article-cientific-sobre-sindrome-neuro-cranio-vertebral-associada-sindrome-dehlers-danlos","status":"publish","type":"comunicacion","link":"https:\/\/institutchiaribcn.com\/ca\/nou-article-cientific-sobre-sindrome-neuro-cranio-vertebral-associada-sindrome-dehlers-danlos\/","title":{"rendered":"Nou article cient\u00edfic sobre la S\u00edndrome Neuro-Cranio-vertebral associada  a la S\u00edndrome d\u2019Ehlers-Danlos"},"content":{"rendered":"<p class=\"text-muted aniview centerTXT\">Publicat per\u00a0<a title=\"Entrades de ICSEB\" href=\"https:\/\/institutchiaribcn.com\/ca\/author\/chiari\/\" rel=\"author\">ICSEB<\/a>\u00a0el 30 maig, 2025<\/p>\n<p>&nbsp;<\/p>\n<p><strong>La S\u00edndrome de Ehlers-*Danlos (EDS)\u00a0<\/strong>inclou un grup complex de trastorns heterogenis, amb car\u00e0cter hereditari, caracteritzats per la fragilitat i augment d\u2019elasticitat dels teixits connectius tous, que ens concerneix especialment respecte al<strong>\u00a0tipus amb patologia vertebral i inestabilitat craniocervical.<\/strong><\/p>\n<p><em>Quina relaci\u00f3 tenen la S\u00edndrome de Ehlers-Danlos (EDS) i la S\u00edndrome Neuro-cranio-vertebral (SNCV)?<\/em><\/p>\n<p><em>Eliminar la tracci\u00f3 del Filum terminale mitjan\u00e7ant el tractament del Filum System\u00ae pot ajudar als pacients amb Ehlers-*Danlos associat a SNCV?<\/em><\/p>\n<p>El nou article \u201c<strong>Neuro-Cranio-Vertebral Syndrome Associated with Ehlers\u2013Danlos Syndrome: Diagnosi and Treatment\u201d<\/strong>, publicat per\u00a0<strong>Miguel B. Royo-Salvador , Marco V. Fiallos-Rivera i Horia C. Salca<\/strong>, intenta respondre a aquestes preguntes, proposant fer-ho mitjan\u00e7ant la teoria de la S\u00edndrome Neuro-cranio-vertebral en relaci\u00f3 a la disfunci\u00f3 del col\u00b7lagen en el Filum Terminale per la EDS, i el conseg\u00fcent tractament.<\/p>\n<p>En la publicaci\u00f3 a Biomed es considera que l\u2019elasticitat sobre la columna vertebral causa una elongaci\u00f3 major que la del Filum terminale, per la qual cosa aquesta \u00faltima s\u2019esgota i acaba en una tracci\u00f3 caudal del Sistema Nervi\u00f3s Central; i amb aix\u00f2 en una s\u00edndrome Neuro-cranio-vertebral.<\/p>\n<p>Els autors descriuen per primera vegada els resultats observats en un grup de pacients operats a l\u2019 ICSEB amb el doble diagn\u00f2stic de EDS i SNCV, en comparaci\u00f3 amb un grup de malalts nom\u00e9s amb SNCV.<\/p>\n<p>Segons els autors, els pacients de la mostra amb EDS i SNCV van presentar m\u00e9s s\u00edmptomes cranials i vertebrals que l\u2019altre grup. Tamb\u00e9 es van observar difer\u00e8ncies significatives en els signes neurol\u00f2gics presents en la EDS-SNCV en comparaci\u00f3 amb aquells \u00fanicament amb SNCV. A m\u00e9s,<strong>\u00a0els pacients sotmesos a secci\u00f3 del filum terminale (SFT) amb la t\u00e8cnica m\u00ednimament invasiva del Filum System\u00ae, van mostrar una millora significativa dels signes i s\u00edmptomes\u00a0<\/strong>(<em>Fig.1<\/em>).<\/p>\n<div align=\"center\"><a href=\"https:\/\/institutchiaribcn.com\/wp-content\/uploads\/2025\/05\/mejorias-improvements-eds-sft-icseb.jpg\"><img decoding=\"async\" class=\"img-responsive alignnone wp-image-9725 size-full\" src=\"https:\/\/institutchiaribcn.com\/wp-content\/uploads\/2025\/05\/mejorias-improvements-eds-sft-icseb.jpg\" alt=\"\" \/><\/a><br \/>\n<em>Fig.1 S\u00edntesi del curs postoperatori en 4 pacients amb SNCV i EDS, operats de SFT. Evoluci\u00f3 dels s\u00edmptomes (A) i evoluci\u00f3 dels signes (B). Verd: desaparici\u00f3\/milloria; groc: sense canvis; vermell: empitjorament.<\/em><em><br \/>\n<\/em><\/div>\n<p>Royo et. Al. destaquen com el\u00a0<strong>concepte d\u2019inestabilitat craniocervical a causa del EDS, llavors, no explica una gran quantitat de signes i s\u00edmptomes neurol\u00f2gics, que en canvi semblen encaixar millor amb la teoria de la tracci\u00f3 vehiculada pel Filum Terminale<\/strong>\u00a0a tot el Sistema Nervi\u00f3s Central en la SNCV.<\/p>\n<p>\u201c<strong>El tractament quir\u00fargic sol implicaria la secci\u00f3 del filum terminale<\/strong>, mentre que la fusi\u00f3 cervical mai estaria justificada en aquests pacients.\u201d, reporten els nostres investigadors com a\u00a0<strong>conclusi\u00f3 de l\u2019estudi.<\/strong><\/p>\n<p>Agra\u00efm a la\u00a0<strong>Chiari &amp; Scoliosis &amp; Syringomyelia Foundation<\/strong>\u00a0per continuar donant suport a la recerca del nostre\u00a0<strong>Departament de R+D+I,\u00a0<\/strong>i a aquest \u00faltim per realitzar un altre estudi tan interessant!<\/p>\n<p>Poden trobar\u00a0<strong>l\u2019article complet<\/strong>\u00a0a:\u00a0<a href=\"https:\/\/institutchiaribcn.com\/ca\/neuro-cranio-vertebral-syndrome-associated-with-ehlers-danlos-syndrome-diagnosis-and-treatment\/\">https:\/\/institutchiaribcn.com\/ca\/neuro-cranio-vertebral-syndrome-associated-with-ehlers-danlos-syndrome-diagnosis-and-treatment\/<\/a><\/p>\n<p>Tamb\u00e9 poden trobar m\u00e9s informaci\u00f3 sobre el EDS en:\u00a0<a href=\"https:\/\/institutchiaribcn.com\/ca\/sindrome-dehlers-danlos\/\">https:\/\/institutchiaribcn.com\/ca\/sindrome-dehlers-danlos\/<\/a><\/p>\n","protected":false},"featured_media":75966,"template":"","tipos-de-comunicacion":[509],"class_list":["post-75965","comunicacion","type-comunicacion","status-publish","has-post-thumbnail","hentry","tipos-de-comunicacion-noticies"],"yoast_head":"<!-- This site is optimized with the Yoast SEO plugin v27.1.1 - https:\/\/yoast.com\/product\/yoast-seo-wordpress\/ -->\n<title>Article cient\u00edfic Sindrome Ehlers\u2011Danlos i SNCV | ICSEB<\/title>\n<meta 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